超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
欧美色视频在线播放,精品国产乱码久久久久久蜜臀,香蕉污视频在线观看
首頁 > 產品中心 > 一抗 > 產品信息
Adracalin Rabbit pAb (bs-11807R)  
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
50ul/1180.00元
100ul/1980.00元
200ul/2800.00元
大包裝/詢價
產品編號 bs-11807R
英文名稱 Adracalin Rabbit pAb
中文名稱 Allgrove綜合征相關蛋白抗體
別    名 AAA; AAAS; AAASb; Achalasia adrenocortical insufficiency alacrimia(Allgrove triple A); Achalasia adrenocortical insufficiency alacrimia; ADRACALA; Aladin; Allgrove triple A; DKFZp586G1624; GL003; AAAS_HUMAN.  
研究領域 細胞生物  免疫學  發育生物學  神經生物學  細胞類型標志物  
抗體來源 Rabbit
克隆類型 Polyclonal
克 隆 號
交叉反應 (predicted: Human,Mouse,Rat,Cow)
產品應用 WB=1:500-2000,IHC-P=1:100-500,IHC-F=1:100-500,IF=1:100-500,ICC/IF=1:100-500,ELISA=1:5000-10000
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
理論分子量 60 kDa
檢測分子量
細胞定位 細胞核 
性    狀 Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human Adracalin: 51-150/546 
亞    型 IgG
純化方法 affinity purified by Protein A
緩 沖 液 0.01M TBS (pH7.4) with 1% BSA, 0.02% Proclin300 and 50% Glycerol.
保存條件 Shipped at 4℃. Store at -20℃ for one year. Avoid repeated freeze/thaw cycles.
注意事項 This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
PubMed PubMed
產品介紹 Aladin (Adracalin) belongs to a family of WD repeat-containing proteins. These proteins have a wide variety of functions, including signal transduction regulation, RNA processing and transcription. Aladin plays a role in peripheral and central nervous system development. It is widely expressed, with the highest expression seen in pituitary gland, corpus callosum, cerebellum, adrenal gland and gastrointestinal structures. Defects in Aladin cause the autosomal recessive disorder achalasia-addisonianism-alacrima (triple A) syndrome. Triple A syndrome is characterized by achalasia, alacrima and adrenocortico-tropin-resistant adrenal insufficiency. Robust expression in neural systems associated with cognitive, motor and sensory functions is consistent with the myriad of symptoms experienced by patients with triple A syndrome.

Function:
Adracalin (AAAS) is expressed in both neuroendocrine and cerebral structures and may function in the normal development of the peripheral and central nervous system. It localizes to nuclear pore complexes (NPCs), large multiprotein assemblies that are the sole sites of nucleocytoplasmic transport. Defects in AAAS are the cause of achalasia-addisonianism-alacrima syndrome (AAA syndrome); also known as triple-A syndrome or Allgrove syndrome.

Subcellular Location:
nuclear pore

Tissue Specificity:
Widely expressed. Particularly abundant expression is found in cerebellum, corpus callosum, adrenal gland, pituitary gland, gastrointestinal structures and fetal lung.

DISEASE:
Defects in AAAS are the cause of achalasia-addisonianism-alacrima syndrome (AAAS) [MIM:231550]; also known as triple-A syndrome or Allgrove syndrome. AAAS is an autosomal recessive disorder characterized by adreno-corticotropic hormone (ACTH)-resistant adrenal failure, achalasia of the esophageal cardia and alacrima. The syndrome is associated with variable and progressive neurological impairment involving the central, peripheral, and autonomic nervous system. Other features such as palmoplantar hyperkeratosis, short stature, facial dysmorphy and osteoporosis may also be present.

Similarity:
Contains 4 WD repeats.

SWISS:
Q9NRG9

Gene ID:
8086

Database links:

Entrez Gene: 8086 Human

Entrez Gene: 223921 Mouse

Entrez Gene: 300259 Rat

Omim: 605378 Human

SwissProt: Q9NRG9 Human

SwissProt: P58742 Mouse

Unigene: 369144 Human

Unigene: 352946 Mouse

Unigene: 104730 Rat



版權所有 2004-2026 www.ggggww.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 艳母1-6在线播放 | 精品无人区一线二线三线区别 | 国产女色| 日日干夜夜草 | 夜夜躁狠狠躁日日躁麻豆老人 | 日韩乱码在线观看 | 成年女人永久免费观看视频 | 色婷婷精品久久二区二区我来 | 日本成本人三级在线观看 | 国产精品影院在线观看 | 成人av网站在线播放 | 九九精品超级碰视频 | 扒开双腿疯狂进出爽爽爽动态图 | 97视频免费在线观看 | 午夜福利啪啪体验区 | 91夜色| 欧美亚洲在线视频 | 高清国产AV一区二区三区 | 中文字幕无码精品亚洲资源网久久 | 亚洲国产成人乱码 | 国产丰满老熟女一区二区三区 | 天天躁人人躁人人躁狂躁 | 在线观看自拍 | 天天天做夜夜夜做无码 | 国产色欲色欲色欲WWW | 天堂久久久久久 | 久久久久免费网站 | 精品国产黄a∨片高清在线 欧美日韩精品综合 | 中国产xxxxa片在线观看 | 亚洲日韩精品无码av海量 | 一区二区三级视频 | 女人和公猪交内射网站 | 国产99视频精品免费观看9 | 内射精品无码中文字幕 | 欲香欲色天天综合和网 | 老司机亚洲精品 | 午在线亚洲男人午在线 | 国产亚洲av片在线观看18女人 | 成年人天堂 | 国产黄色录像片 | 精品一久久 |