超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
伊人久久免费视频,51自拍视频,免费a级毛片又大又粗又黑
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-BMPR1B/PE-Cy5 Conjugated antibody (bs-6639R-PE-Cy5)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-6639R-PE-Cy5
英文名稱 Rabbit Anti-BMPR1B/PE-Cy5 Conjugated antibody
中文名稱 PE-Cy5標記的骨形態發生蛋白受體1B抗體
別    名 BMPR-IB; Activin receptor like kinase 6; Acvrlk6; ALK 6; ALK6; alk6tr; BMP type-1B receptor; BMPR IB; BMPR-1B; Bmpr1b; BMPRIB; BMR1B_HUMAN; Bone morphogenetic protein receptor type 1B; Bone morphogenetic protein receptor type IB; Bone morphogenetic protein receptor type-1B; BR 1b; BR1b; CDw 293; CDw293; CDw293 antigen; CFK 43a; CFK43a; Serine/threonine receptor kinase; zALK 6; zALK6.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 細胞生物  信號轉導  干細胞  轉錄調節因子  激酶和磷酸酶  細胞表面分子  細胞外基質  表觀遺傳學  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 (predicted: Human, Mouse, Rat, Dog, Cow, Rabbit, Sheep, .)
產品應用
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 56kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human BMPR1B
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
On ligand binding, forms a receptor complex consisting of two type II and two type I transmembrane serine/threonine kinases. Type II receptors phosphorylate and activate type I receptors which autophosphorylate, then bind and activate SMAD transcriptional regulators. Receptor for BMP7/OP-1 and GDF5.
Involvement in disease; Defects in BMPR1B are the cause of acromesomelic chondrodysplasia with genital anomalies (AMDGA). Acromesomelic chondrodysplasias are rare hereditary skeletal disorders characterized by short stature, very short limbs, and hand/foot malformations. The severity of limb abnormalities increases from proximal to distal with profoundly affected hands and feet showing brachydactyly and/or rudimentary fingers (knob-like fingers).
Defects in BMPR1B are a cause of brachydactyly type A2 (BDA2) [MIM:112600]. Brachydactylies (BDs) are a group of inherited malformations characterized by shortening of the digits due to abnormal development of the phalanges and/or the metacarpals. They have been classified on an anatomic and genetic basis into five groups, A to E, including three subgroups (A1 to A3) that usually manifest as autosomal dominant traits. BDA2 was described first in a large Norwegian kindred. BDA2 is caused by mutations in BMPR1B gene and studies demonstrate that these mutations function as dominant negatives in vitro and in vivo.

Function:
On ligand binding, forms a receptor complex consisting of two type II and two type I transmembrane serine/threonine kinases. Type II receptors phosphorylate and activate type I receptors which autophosphorylate, then bind and activate SMAD transcriptional regulators. Receptor for BMP7/OP-1 and GDF5.

Subcellular Location:
Membrane; Single-pass type I membrane protein.

DISEASE:
Defects in BMPR1B are the cause of acromesomelic chondrodysplasia with genital anomalies (AMDGA) [MIM:609441]. Acromesomelic chondrodysplasias are rare hereditary skeletal disorders characterized by short stature, very short limbs, and hand/foot malformations. The severity of limb abnormalities increases from proximal to distal with profoundly affected hands and feet showing brachydactyly and/or rudimentary fingers (knob-like fingers).
Defects in BMPR1B are a cause of brachydactyly type A2 (BDA2) [MIM:112600]. Brachydactylies (BDs) are a group of inherited malformations characterized by shortening of the digits due to abnormal development of the phalanges and/or the metacarpals. They have been classified on an anatomic and genetic basis into five groups, A to E, including three subgroups (A1 to A3) that usually manifest as autosomal dominant traits. BDA2 was described first in a large Norwegian kindred. BDA2 is caused by mutations in BMPR1B gene and studies demonstrate that these mutations function as dominant negatives in vitro and in vivo.

Similarity:
Belongs to the protein kinase superfamily. TKL Ser/Thr protein kinase family. TGFB receptor subfamily.
Contains 1 GS domain.
Contains 1 protein kinase domain.

Database links:

Entrez Gene: 658 Human

Entrez Gene: 12167 Mouse

Omim: 603248 Human

SwissProt: O00238 Human

SwissProt: P36898 Mouse

Unigene: 598475 Human

Unigene: 39089 Mouse



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.ggggww.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 影音先锋在线中文字幕 | 在线观看av一区 | 成人爽爽 | 国产高清视频免费观看 | 亚洲成A∨人片在无码2023 | 国产在线播放观看 | 五月天色av | 边啃奶头边躁狠狠躁玩爽在水里面 | 久久青青无码AV亚洲黑人 | av污在线观看 | 欧美顶级METART裸体全部自慰 | 日本不卡一区二区三区在线 | 亚洲精品久久久久一区二区三区 | VIDEOS日本熟妇人妻多毛 | 在线观看日本高清二区 | 啊灬啊灬啊灬快灬A片免费 亚洲不卡一区二区三区 | 日本a不卡 | 中文字幕欧美日韩va免费视频 | 欧美激情自拍偷拍 | 日韩一级黄色片 | 国产精品久久久久久久久久综合 | 久久国产精品影视 | 337P日本欧洲亚洲大胆 | 亚洲成A人一区二区三区 | 精品国精品国产自在久国产应用 | 天天躁夜夜躁狠狠躁2021 | www.俺高潮了.com | 国产一二三四区在线 | 国产精品三区www17con | 色噜噜色狠狠狠狠狠综合色一 | 亚洲一区二区欧美日韩 | 国产精品一区二区精品视频免费看 | 伊人无码一区二区三区 | 亚洲热视频在线观看 | 欧美黄页在线免费观看 | 成人无码www免费视频嘿嘿软件 | 欧美日一 | 亚洲码国产精品高潮在线 | 亚洲一区二区三区写真 | 亚洲AV无码一区二区三区系列 | 久久99精品国产.久久久久 |