超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關(guān)注公眾號           掃碼咨詢技術(shù)支持           掃碼咨詢技術(shù)服務(wù)
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  關(guān)于我們  聯(lián)系我們
亚洲精品在线视频播放,亚洲精品午夜国产va久久成人,国产网站在线
Rabbit Anti-HMGCS2/HRP Conjugated antibody (bs-5070R-HRP)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術(shù)支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產(chǎn)品編號 bs-5070R-HRP
英文名稱 Rabbit Anti-HMGCS2/HRP Conjugated antibody
中文名稱 辣根過氧化物酶標(biāo)記的三羥基三甲基輔酶A合成酶2抗體
別    名 3 hydroxy 3 methylglutaryl Coenzyme A synthase 2 (mitochondrial); 3 hydroxy 3 methylglutaryl Coenzyme A synthase 2; 3 hydroxy 3 methylglutaryl coenzyme A synthase; 3-hydroxy-3-methylglutaryl coenzyme A synthase; HMCS2_HUMAN; HMG CoA synthase; HMG-CoA synthase; HMGCS 2; HMGCS2; Hydroxymethylglutaryl CoA synthase; Hydroxymethylglutaryl CoA synthase mitochondrial; Hydroxymethylglutaryl-CoA synthase; mitochondrial.  
規(guī)格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領(lǐng)域 腫瘤  心血管  細(xì)胞生物  免疫學(xué)  信號轉(zhuǎn)導(dǎo)  脂蛋白  線粒體  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應(yīng) (predicted: Human, Mouse, Rat, Dog, Pig, Cow, Horse, Rabbit, )
產(chǎn)品應(yīng)用 WB=1:500-2000 ELISA=1:100-1000 IHC-P=1:50-200 IHC-F=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 52kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human HMGCS2
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
HMGCS2 is a mitochondrial enzyme that catalyzes the first reaction of ketogenesis, a metabolic pathway that provides lipid-derived energy for various organs during times of carbohydrate deprivation, such as fasting. Mutations in this gene are associated with HMG-CoA synthase deficiency. Alternatively spliced transcript variants encoding different isoforms have been found for this gene.

Function:
This enzyme condenses acetyl-CoA with acetoacetyl-CoA to form HMG-CoA, which is the substrate for HMG-CoA reductase.

Subcellular Location:
Mitochondrion.

Tissue Specificity:
High expression in liver and colon. Low expression in testis, heart, skeletal muscle and kidney.

DISEASE:
Defects in HMGCS2 are the cause of HMG-CoA synthase deficiency (HMGCS deficiency) [MIM:605911]; also known as deficiency of mitochondrial 3-hydroxy-3-methylglutaryl-CoA synthase 2. Affected individuals present with severe hypoketotic hypoglycemia, mild hepatomegaly, or fatty liver, and a nondiagnostic pattern of urinary organic acids with increase of medium and short chain dicarboxylic acids.

Similarity:
Belongs to the HMG-CoA synthase family.

Database links:
UniProtKB/Swiss-Prot: P54868.1

Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.

版權(quán)所有 2004-2026 www.ggggww.cn 北京博奧森生物技術(shù)有限公司
通過國際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網(wǎng)安備110107000727號
主站蜘蛛池模板: 婷婷色播婷婷 | 国产良心大作白丝精厕 | 亚洲精品国产一区二区 | 国产91视频在线 | 日韩久久久久久久久 | 网站一区 | 性生交大片免费看图片 | 日本播放一区二区 | 极情综合网| 精品久久久久久久久久国产潘金莲 | 日本免费一区二区三区最新 | 亚洲va无码va在线va天堂 | 亚洲精品一卡二卡三卡四卡2021 | 欧美日韩久久久精品A片妖精 | 精品自拍一区 | 国产成人精品久久久一区二区三区 | 日本在线观看中文自拍 | 欧美性高潮 | 女人牲交视频一级毛片 | 铠甲勇士第一部52集全 | 成全视频在线观看免费高清在线观看 | FREEZEFRAME丰满老妇 | 免费XXXX大片 | 91亚洲成a人片在线观看www | 国产a级理论片无码老男人 午夜视频在线观看一区二区 | 日本视频在线观看免费 | www.三区 | 国产亚洲中字幕欧 | 免费一区在线观看 | 国产精品视频免费一区二区 | 国产精品最新乱视频二区 | 日韩美女在线 | 亚洲欧美日本国产 | 无码国产精品免费看 | 国产亚洲日韩欧美另类第八页 | 国产精品久久久久77777丨 | 伊波拉病毒在线观看超清国语 | 中文字幕第一页卡通动漫在线 | 日日噜噜噜夜夜爽爽狠狠小说 | 亚洲AV无码午夜国产精品色软件 | 久久一区二区三区国产精品 |