超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
免费一看一级毛片,欧美三级不卡在线播放,中国亚洲呦女专区
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-FECH/Biotin Conjugated antibody (bs-9521R-Bio)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-9521R-Bio
英文名稱 Rabbit Anti-FECH/Biotin Conjugated antibody
中文名稱 生物素標記的鐵螯合酶抗體
別    名 EPP; FCE; Ferrochelatase (protoporphyria); Ferrochelatase; Ferrochelatase mitochondrial; Heme synthetase; Protoheme ferro lyase; HEMH_HUMAN.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 心血管  細胞生物  免疫學  細胞類型標志物  細胞骨架  線粒體  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 (predicted: Human, Mouse, Rat, Dog, Pig, Cow, Horse, Sheep, )
產品應用 WB=1:50-200 ELISA=1:100-1000 IHC-P=1:50-200 IHC-F=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 43kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human EPB41
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
Ferrochelatase catalyzes the insertion of the ferrous form of iron into protoporphyrin IX in the heme synthesis pathway, and is localised in the mitochondrion. Defects in ferrochelatase are associated with protoporphyria. Two transcript variants encoding different isoforms have been found for this gene. Porphyrias are a group of inherited or acquired disorders of certain enzymes in the heme biosynthetic pathway (also called porphyrin pathway). They are broadly classified as hepatic porphyrias or erythropoietic porphyrias, based on the site of the overproduction and mainly accumulation of the porphyrins (or their chemical precursors). They manifest with either skin problems, or neurological complications, or occasionally both.

Function:
Catalyzes the ferrous insertion into protoporphyrin IX.

Subunit:
Homodimer.

Subcellular Location:
Mitochondrion inner membrane; Peripheral membrane protein; Matrix side.

DISEASE:
Defects in FECH are the cause of erythropoietic protoporphyria (EPP) [MIM:177000]. Porphyrias are inherited defects in the biosynthesis of heme, resulting in the accumulation and increased excretion of porphyrins or porphyrin precursors. They are classified as erythropoietic or hepatic, depending on whether the enzyme deficiency occurs in red blood cells or in the liver. EPP is a form of porphyria marked by excessive protoporphyrin in erythrocytes, plasma, liver and feces, and by widely varying photosensitive skin changes ranging from a burning or pruritic sensation to erythema, edema and wheals.

Similarity:
Belongs to the ferrochelatase family.

Database links:

Entrez Gene: 2235 Human

Omim: 612386 Human

SwissProt: P22830 Human

Unigene: 365365 Human



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.ggggww.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 18禁男女污污污午夜网站免费暖暖 | 免费无码又爽又刺激高潮的视频 | 国产特色特黄的视频免费观看 | 综合欧美亚洲日本少妇 | 东京久久久 | 插插天天 | 免费看91视频 | 超碰九色| 97人妻免费碰视频碰免 | 久久成人影视 | 色播久久人人爽人人爽人人片av | www.亚洲国产 | 国产性VIDEOSGRATIS喷潮 | 免费在线观看成人 | 精品不卡在线 | 国内精品国产三级国产在线专 | 一区二区成人精品 | 欧美aaa一级片 | 蜜桃国精产品二三三区视频 | 一区二区三区免费观看 | 99久久精品久久 | 亚洲色无码中文字幕在线 | 精品免费av| 国产学生系列一区二区三区 | 阳茎进去女人阳道视频特黄 | 一级毛片大片 | 延禧攻略在线看 | 亚洲视频国产一区 | 狠狠躁夜夜躁青青草原 | 激情二区| 久久亚洲综合色 | av最新在线观看 | 国产精品日产三级在线 | 福利视频10000 | 男人a天堂2814 | 少妇被黑人4P到惨叫 | 天天干天天操天天舔 | 亚洲欧美日韩中文视频 | 欧美三区二区一区 | 日本高清视频免费看 | 欧美激情精品 |