超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
亚洲一级黄色录像,亚洲最大成人综合,久久久久精
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-FECH/Cy3 Conjugated antibody (bs-9521R-Cy3)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-9521R-Cy3
英文名稱 Rabbit Anti-FECH/Cy3 Conjugated antibody
中文名稱 Cy3標記的鐵螯合酶抗體
別    名 EPP; FCE; Ferrochelatase (protoporphyria); Ferrochelatase; Ferrochelatase mitochondrial; Heme synthetase; Protoheme ferro lyase; HEMH_HUMAN.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 心血管  細胞生物  免疫學  細胞類型標志物  細胞骨架  線粒體  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 (predicted: Human, Mouse, Rat, Dog, Pig, Cow, Horse, Sheep, )
產品應用 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 43kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human EPB41
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
Ferrochelatase catalyzes the insertion of the ferrous form of iron into protoporphyrin IX in the heme synthesis pathway, and is localised in the mitochondrion. Defects in ferrochelatase are associated with protoporphyria. Two transcript variants encoding different isoforms have been found for this gene. Porphyrias are a group of inherited or acquired disorders of certain enzymes in the heme biosynthetic pathway (also called porphyrin pathway). They are broadly classified as hepatic porphyrias or erythropoietic porphyrias, based on the site of the overproduction and mainly accumulation of the porphyrins (or their chemical precursors). They manifest with either skin problems, or neurological complications, or occasionally both.

Function:
Catalyzes the ferrous insertion into protoporphyrin IX.

Subunit:
Homodimer.

Subcellular Location:
Mitochondrion inner membrane; Peripheral membrane protein; Matrix side.

DISEASE:
Defects in FECH are the cause of erythropoietic protoporphyria (EPP) [MIM:177000]. Porphyrias are inherited defects in the biosynthesis of heme, resulting in the accumulation and increased excretion of porphyrins or porphyrin precursors. They are classified as erythropoietic or hepatic, depending on whether the enzyme deficiency occurs in red blood cells or in the liver. EPP is a form of porphyria marked by excessive protoporphyrin in erythrocytes, plasma, liver and feces, and by widely varying photosensitive skin changes ranging from a burning or pruritic sensation to erythema, edema and wheals.

Similarity:
Belongs to the ferrochelatase family.

Database links:

Entrez Gene: 2235 Human

Omim: 612386 Human

SwissProt: P22830 Human

Unigene: 365365 Human



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.ggggww.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 欧美日韩a级片 | 日本添下边无码视频全过程 | 欧美性猛交xxxx乱大交蜜桃 | 黑人成人网 | 男人插女人骚视频 | 午夜三级视频 | 国产91丝袜香蕉在线播放 | 四虎影视黄色 | 老妇女色视频 | 成人18毛片 | 国产91精品欧美 | 国产三级精品片 | 一级猛片免费看 | 国产精品啪一品二区三区粉嫩 | 欧美日韩一本的免费高清视频 | 欧美日韩国产成人在线91 | 9色porny自拍视频一区二区 | 一本色道久久88亚洲精品综合 | 亚洲一二三四区不卡 | 99热国产在线手机精品 | 偷拍成人一区亚洲欧美 | 天堂蜜桃一区二区三区 | 亚洲国产成人久久久 | 99视频一区二区三区 | 丰满少妇被猛烈进入A片 | 日韩精品在线观 | 色97色 | 国产欧美日韩综合精品二区 | 日本欧美一级aaaaa毛片 | 一本色道久久亚洲综合精品蜜桃 | 又色又爽又黄又免费的视频网站 | 天天摸天天透天天添 | 国产欧美日韩在线在线播放 | 日本网站一区 | 脱了我奶罩亲我奶头好舒服 | 377人体裸体露私图片 | a级片在线免费观看视频 | 亚洲国产在 | 国产精品日产三级在线 | 高清中文字幕在线 | 中文字幕乱码人妻系列 |