超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
欧美一区二区三区久久久,亚洲永久免费观看,91宅男噜噜噜66在线观看
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-FECH/PE Conjugated antibody (bs-9521R-PE)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-9521R-PE
英文名稱 Rabbit Anti-FECH/PE Conjugated antibody
中文名稱 PE標記的鐵螯合酶抗體
別    名 EPP; FCE; Ferrochelatase (protoporphyria); Ferrochelatase; Ferrochelatase mitochondrial; Heme synthetase; Protoheme ferro lyase; HEMH_HUMAN.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 心血管  細胞生物  免疫學  細胞類型標志物  細胞骨架  線粒體  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 (predicted: Human, Mouse, Rat, Dog, Pig, Cow, Horse, Sheep, )
產品應用 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 43kDa
細胞定位 細胞膜 線粒體
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human EPB41
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
Ferrochelatase catalyzes the insertion of the ferrous form of iron into protoporphyrin IX in the heme synthesis pathway, and is localised in the mitochondrion. Defects in ferrochelatase are associated with protoporphyria. Two transcript variants encoding different isoforms have been found for this gene. Porphyrias are a group of inherited or acquired disorders of certain enzymes in the heme biosynthetic pathway (also called porphyrin pathway). They are broadly classified as hepatic porphyrias or erythropoietic porphyrias, based on the site of the overproduction and mainly accumulation of the porphyrins (or their chemical precursors). They manifest with either skin problems, or neurological complications, or occasionally both.

Function:
Catalyzes the ferrous insertion into protoporphyrin IX.

Subunit:
Homodimer.

Subcellular Location:
Mitochondrion inner membrane; Peripheral membrane protein; Matrix side.

DISEASE:
Defects in FECH are the cause of erythropoietic protoporphyria (EPP) [MIM:177000]. Porphyrias are inherited defects in the biosynthesis of heme, resulting in the accumulation and increased excretion of porphyrins or porphyrin precursors. They are classified as erythropoietic or hepatic, depending on whether the enzyme deficiency occurs in red blood cells or in the liver. EPP is a form of porphyria marked by excessive protoporphyrin in erythrocytes, plasma, liver and feces, and by widely varying photosensitive skin changes ranging from a burning or pruritic sensation to erythema, edema and wheals.

Similarity:
Belongs to the ferrochelatase family.

Database links:

Entrez Gene: 2235 Human

Omim: 612386 Human

SwissProt: P22830 Human

Unigene: 365365 Human



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.ggggww.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 人妻AV无码一区二区三区 | 久久精品国产一区二区无码 | 在线免费av观看 | 国产婷婷色综合av蜜臀av | 末发育女AV片一区二区 | 国产999精品久久久久久绿帽 | 亚州精品久久久久久久久 | 在线中文字幕网 | 国产黄色片免费 | 国产精品涩涩涩视频网站 | 理论片午午伦夜理片影院99 | 91蜜桃臀久久一区二区 | 天啦噜国产精品亚洲精品 | 亚洲清纯国产 | 黑人大荫道BBWBBB高潮潮喷 | 偷拍视频网站 | 日本久热 | 成片人免费观看一级A片 | 亚洲日韩偷拍丝袜综合 | 视频一区二区精品 | 久久久国产AV | 亚洲人成网线在线播放VA蜜芽 | 婷婷色播婷婷 | www.999精品 | 伦乱av| 国产亚洲精久久久久久无码77777 | 欧美综合色网 | 中文字幕第三区 | 亚州精品av久久久久久久影院 | 激情内射日本一区二区三区 | 少妇做爰免费视频网站裸体艺术 | 欧美一级淫片a | 国产资源免费观看 | 青春草视频在线播放 | 国产精品久久久久久久白皙女 | 日本一道本线一区免费 | 久久久久久久久久久国产 | 99在线精品视频免费观看20 | 2019一级黄色毛片免费看网 | www.久久综合| 精品一区二区av |