超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯(lián)系我們
亚洲六九视频,亚洲色大成网站WWW永久,免费的色视频
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-FECH/PE-Cy3 Conjugated antibody (bs-9521R-PE-Cy3)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-9521R-PE-Cy3
英文名稱 Rabbit Anti-FECH/PE-Cy3 Conjugated antibody
中文名稱 PE-Cy3標記的鐵螯合酶抗體
別    名 EPP; FCE; Ferrochelatase (protoporphyria); Ferrochelatase; Ferrochelatase mitochondrial; Heme synthetase; Protoheme ferro lyase; HEMH_HUMAN.  
規(guī)格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 心血管  細胞生物  免疫學  細胞類型標志物  細胞骨架  線粒體  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 (predicted: Human, Mouse, Rat, Dog, Pig, Cow, Horse, Sheep, )
產品應用 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 43kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human EPB41
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
Ferrochelatase catalyzes the insertion of the ferrous form of iron into protoporphyrin IX in the heme synthesis pathway, and is localised in the mitochondrion. Defects in ferrochelatase are associated with protoporphyria. Two transcript variants encoding different isoforms have been found for this gene. Porphyrias are a group of inherited or acquired disorders of certain enzymes in the heme biosynthetic pathway (also called porphyrin pathway). They are broadly classified as hepatic porphyrias or erythropoietic porphyrias, based on the site of the overproduction and mainly accumulation of the porphyrins (or their chemical precursors). They manifest with either skin problems, or neurological complications, or occasionally both.

Function:
Catalyzes the ferrous insertion into protoporphyrin IX.

Subunit:
Homodimer.

Subcellular Location:
Mitochondrion inner membrane; Peripheral membrane protein; Matrix side.

DISEASE:
Defects in FECH are the cause of erythropoietic protoporphyria (EPP) [MIM:177000]. Porphyrias are inherited defects in the biosynthesis of heme, resulting in the accumulation and increased excretion of porphyrins or porphyrin precursors. They are classified as erythropoietic or hepatic, depending on whether the enzyme deficiency occurs in red blood cells or in the liver. EPP is a form of porphyria marked by excessive protoporphyrin in erythrocytes, plasma, liver and feces, and by widely varying photosensitive skin changes ranging from a burning or pruritic sensation to erythema, edema and wheals.

Similarity:
Belongs to the ferrochelatase family.

Database links:

Entrez Gene: 2235 Human

Omim: 612386 Human

SwissProt: P22830 Human

Unigene: 365365 Human



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.ggggww.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫(yī)療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 亚洲天堂福利视频 | 亚洲成av人片在线观看麦芽 | 中文精品一卡2卡3卡4卡国色 | 二区国产 | 麻豆熟妇人妻XXXXXX | 成年人网站免费视频 | 欧美中文字幕在线观看 | 2021年国产精品每日更新 | 黄网站免费久久 | 国产吃瓜黑料一区二区 | 欧美成人免费一级人片100 | 国产欧美久久高清 | 久久精品视频一区二区三区 | 丰满人妻一区二区三区无码av | 无码国产午夜福利片在线观看 | 韩国精品一区二区三区无码视频 | 97豆奶视频国产 | 国产成人愉拍免费视频 | 欧美国产精品天堂 | 日韩av免费在线看 | 一级毛片在线免费观看视频 | 双腿张开被9个男人调教 | 国产精品女A片爽爽波多野结衣 | 超碰一区 | 国产公开免费人成视频 | 麻豆入口国产精品 | 国产精品无码免费热播 | 91麻豆精品国产91久久久使用方法 | 免费一级特黄录像 | 欧美精品九九99久久 | 精品二区在线 | 91精产国品一二三区在线观看 | 亚洲国产一区二区精品视频 | 国产一区91 | 国产精品一品二区三区四区18 | 一本之道无码一区二区 | 天天摸天天操天天干 | 青青草成人免费 | 国产成人无码精品久久久小说 | 久久嫩草精品久久久久 | 中日韩欧美在线观看 |