超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
国产∨亚洲V天堂无码久久久,蜜桃精品一区二区,婷婷色香合缴缴情av第三区
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-KBP/BF555 Conjugated antibody (bs-9716R-BF555)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-9716R-BF555
英文名稱 Rabbit Anti-KBP/BF555 Conjugated antibody
中文名稱 BF555標記的KBP蛋白抗體
別    名 Hypothetical protein LOC26128; KBP; KBP_HUMAN; KIAA1279; KIF1-binding protein; TTC20; Uncharacterized protein KIAA1279.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 細胞生物  免疫學  信號轉導  細胞周期蛋白  細胞分化  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 Human,  (predicted: Mouse, Rat, Horse, )
產品應用 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 72kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human KBP
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
Chromosome 10 contains over 800 genes and 135 million nucleotides, making up nearly 4.5% of the human genome. PTEN is an important tumor suppressor gene located on chromosome 10 and, when defective, causes a genetic predisposition to cancer development known as Cowden syndrome. The chromosome 10 encoded gene ERCC6 is important for DNA repair and is linked to Cockayne syndrome which is characterized by extreme photosensitivity and premature aging. Tetrahydrobiopterin deficiency and a number of syndromes involving defective skull and facial bone fusion are also linked to chromosome 10. As with most trisomies, trisomy 10 is rare and is deleterious. The KIAA1279 gene product has been provisionally designated KIAA1279 pending further characterization.

Function:
Required for organization of axonal microtubules, andaxonal outgrowth and maintenance during peripheral and centralnervous system development. Regulates mitochondrial transport bymodulating KIF1B motor activity.

Subunit:
Interacts with KIF1B.

Subcellular Location:
Mitochondrion.

Tissue Specificity:
Highly expressed in heart, brain, ovary, testis, spinal cord and all specific brain regions examined. Moderate expressed at intermediate level in all other adult tissues examined, as well as in fetal liver and brain. Not expressed in blood leukocytes.

DISEASE:
Defects in KIAA1279 are the cause of Goldberg-Shprintzenmegacolon syndrome (GOSHS) [MIM:609460]. GOSHS is characterized bymicrocephaly, mental retardation and facial dysmorphism, as well asphenotypes related to Hirschsprung disease syndrome.

Similarity:
Belongs to the KIF1-binding protein family.

Database links:

Entrez Gene: 100063227 Horse

Entrez Gene: 26128 Human

Entrez Gene: 72320 Mouse

Entrez Gene: 606294 Rat

Omim: 609367 Human

SwissProt: Q96EK5 Human

SwissProt: Q6ZPU9 Mouse

SwissProt: Q4G074 Rat

Unigene: 279580 Human

Unigene: 258955 Mouse

Unigene: 100975 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.ggggww.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 欧美性猛交xxxx偷拍洗澡 | 91精品国产一区二区三密臀 | 无码国产精品一区二区VR老人 | 中文字幕色婷婷在线视频 | 国产小视频在线观看 | 91成人入口 | 欧美aaa一级片 | 国产精自产拍久久久久久蜜 | AV永久天堂一区二区三区香港 | 91天天色| 欧美一级淫片a免费播放口 日韩免费一级 | 国产精品一级二级在线观看 | 久久久性生活视频 | 亚洲AV无码一区二区三区18 | 欧美综合二区 | 在教室伦流澡到高潮hgl视频 | 午夜三级视频 | 国产精品久久久999 色婷婷av一区二区三区小说 | 国产一级小视频 | AV在线观看 | 久久精品国产99久久久古代 | 国产69精品久久久久99 | 巜被社长侵犯的人2中文在线 | 国产精品一级毛片在线 | 色欲A∨无码蜜臀AV免费播 | 99久久99久久久精品棕色圆 | 一级做a爰性色毛片免费1 | 国产精品一区二区久久精品爱涩 | 精品国产人免费观看成人片 | a级毛片黄免费a级毛片 | 另类免费视频 | 久久久久无码精品国产 | 无码人妻丰满熟妇啪啪区日韩久久 | 年轻的朋友在线免费观看 | 一级做a爰性色毛片免费1 | 亚洲色大成网站WWW永久男同 | 国产精品久久久久永久免费 | 欧美XXXX做受欧美69 | 一区二区三区四区在线视频 | 日韩人妻无码系列专区 | 亚洲视频无码一区 |