超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關(guān)注公眾號(hào)           掃碼咨詢(xún)技術(shù)支持           掃碼咨詢(xún)技術(shù)服務(wù)
  
客服熱線(xiàn):400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  關(guān)于我們  聯(lián)系我們
亚洲4区,色婷婷综合缴情综免费观看,在线国产精品一区
Rabbit Anti-G6PC3/BF594 Conjugated antibody (bs-13253R-BF594)
訂購(gòu)熱線(xiàn):400-901-9800
訂購(gòu)郵箱:sales@bioss.com.cn
訂購(gòu)QQ:  400-901-9800
技術(shù)支持:techsupport@bioss.com.cn
說(shuō) 明 書(shū): 100ul  
100ul/2980.00元
大包裝/詢(xún)價(jià)
產(chǎn)品編號(hào) bs-13253R-BF594
英文名稱(chēng) Rabbit Anti-G6PC3/BF594 Conjugated antibody
中文名稱(chēng) BF594標(biāo)記的葡萄糖-6-磷酸酶3/G6Pase-β抗體
別    名 G-6-Pase 3; G6Pase 3; G6Pase-beta; Glucose 6 phosphatase, catalytic, 3; Glucose-6-phosphatase 3; Glucose-6-phosphatase beta; SCN4; Ubiquitous glucose-6-phosphatase catalytic subunit-related protein; UGRP;   
規(guī)格價(jià)格 100ul/2980元 購(gòu)買(mǎi)        大包裝/詢(xún)價(jià)
說(shuō) 明 書(shū) 100ul  
研究領(lǐng)域 細(xì)胞生物  信號(hào)轉(zhuǎn)導(dǎo)  糖尿病  新陳代謝  
抗體來(lái)源 Rabbit
克隆類(lèi)型 Polyclonal
交叉反應(yīng)
產(chǎn)品應(yīng)用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 39kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human G6PC3
亞    型 IgG
純化方法 affinity purified by Protein A
儲(chǔ) 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
This gene encodes the catalytic subunit of glucose-6-phosphatase (G6Pase). G6Pase is located in the endoplasmic reticulum (ER) and catalyzes the hydrolysis of glucose-6-phosphate to glucose and phosphate in the last step of the gluconeogenic and glycogenolytic pathways. Mutations in this gene result in autosomal recessive severe congenital neutropenia. Multiple transcript variants have been found for this gene, only one of which is expected to express a protein.[provided by RefSeq, Sep 2009].

Function:
Hydrolyzes glucose-6-phosphate to glucose in the endoplasmic reticulum. May form with the glucose-6-phosphate transporter (SLC37A4/G6PT) a ubiquitously expressed complex responsible for glucose production through glycogenolysis and gluconeogenesis. Probably required for normal neutrophil function.

Subcellular Location:
Endoplasmic reticulum membrane; Multi-pass membrane protein.

Tissue Specificity:
Ubiquitously expressed. Highly expressed in skeletal muscle, at intermediate levels in heart, brain, placenta, kidney, colon, thymus, spleen and pancreas. Also detected in testis, prostate, ovary, liver, lung, small intestine and peripheral blood lymphocytes.

DISEASE:
Defects in G6PC3 are the cause of neutropenia severe congenital autosomal recessive type 4 (SCN4) [MIM:612541]. Autosomal recessive SCN constitutes a primary immunodeficiency syndrome associated with increased apoptosis in myeloid cells. Individuals show a paucity of mature neutrophils in peripheral blood and bone marrow and develop life-threatening bacterial infections. SCN4 is a severe congenital neutropenia syndrome associated with cardiac and urogenital malformations.
Defects in G6PC3 are the cause of Dursun syndrome (DURSS) [MIM:612541]. A disease characterized by pulmonary arterial hypertension, cardiac abnormalities including secundum-type atrial septal defect, intermittent neutropenia, lymphopenia, monocytosis and anemia.

Similarity:
Belongs to the glucose-6-phosphatase family.

Database links:

Entrez Gene: 92579 Human

Entrez Gene: 68401 Mouse

Entrez Gene: 303565 Rat

Omim: 611045 Human

SwissProt: Q9BUM1 Human

SwissProt: Q6NSQ9 Mouse

SwissProt: Q6AZ83 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 www.ggggww.cn 北京博奧森生物技術(shù)有限公司
通過(guò)國(guó)際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書(shū)編號(hào): 00124Q34771R2M/1100
通過(guò)國(guó)際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書(shū)編號(hào): CQC24QY10047R0M/1100
京ICP備05066980號(hào)-1         京公網(wǎng)安備110107000727號(hào)
主站蜘蛛池模板: 男人av的天堂无码专区 | 亚洲伦理在线视频 | 国产美女一级做受老师 | www.青青草.com | 亚洲午夜高清国产拍 | 快看视频在线免费看 | 边摸边脱吃奶边高潮视频免费 | 囯产av无码片毛片一级 | 少妇淫片免费看 | 亲亲草在线视频 | 亚洲精品亚洲人成在线 | 亚洲成av人片 | 一区二区小视频 | 国产成年女人毛片80s网站 | 日韩午夜精品免费理论片 | 日本淫片| 在线无码国产观看播放网址 | 国产亚洲精品无 | 91福利精品第一导航禁漫天堂 | 日本高清一本视频 | 国产精品无码一区二区三区免费 | 一本到国产在线精品国内 | 久久久久久久久久久久中文字幕 | 中文亚洲欧美日韩无线码 | 在线播放免费人成视频在线观看 | 强乱中文字幕亚洲精品 | 国产网战无遮挡 | 黄色一级视频免费观看 | 无码精品国产一区二区三区免费 | 粉嫩av一区二区三区四区五区 | AV永久天堂一区二区三区香港 | 一个人看的www视频免费观看 | 国产帅男男GAY网站视频 | 欧美日韩国产第一页 | 九一视频免费在线观看 | 亚洲最新av无码中文字幕一区 | 人与禽性视频77777交片 | 色中文网 | 国产jizz18高清视频 | 大地资源在线观看免费中文版 | 久久久精品区 |