超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
日韩精品在线播放,日本熟妇色xxxxx日本免费看,国产精品1区2区3区在线观看
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-GCSH/Gold Conjugated antibody (bs-13323R-Gold)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul(10nm  15nm  35nm
100ul/2980.00元
大包裝/詢價
產品編號 bs-13323R-Gold
英文名稱 Rabbit Anti-GCSH/Gold Conjugated antibody
中文名稱 膠體金標記的甘氨酸裂解系統H蛋白抗體
別    名 GCE; GCSH; GCSH_HUMAN; Glycine cleavage system H protein; Glycine cleavage system H protein mitochondrial; Glycine cleavage system protein H (aminomethyl carrier); Glycine cleavage system protein H; Lipoic acid containing protein; mitochondrial; Mitochondrial glycine cleavage system H protein; NKH.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul(10nm  15nm  35nm
研究領域 腫瘤  細胞生物  信號轉導  細胞類型標志物  新陳代謝  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 (predicted: Human, Mouse, Rat, Horse, )
產品應用 IEM=1:20-200 ICA=1:20-200 ChIP=1:20-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 14kDa
性    狀 Lyophilized or Liquid
濃    度 0.4mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human GCSH
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.02M TBS(pH8.2) with 1% BSA, 0.03% Proclin300.
保存條件 Store at 2-8 oC for 3-6 months. Avoid repeated freeze/thaw cycles.
產品介紹 background:
GCSH is a 173 amino acid mitochondrial protein that contains one lipoyl-binding domain and belongs to the gcvH family. Defects in the gene encoding GCSH are the cause of glycine encephalopathy (GCE), an autosomal recessive disease that is also referred to as non-ketotic hyperglycinemia (NKH). Characterized by severe neurological symptoms, patients with GCE have a large amount of glycine accumulated in their body fluids. The gene encoding GCSH maps to human chromosome 16, which encodes over 900 genes and comprises nearly 3% of the human genome.

Function:
The glycine cleavage system catalyzes the degradation of glycine. The H protein shuttles the methylamine group of glycine from the P protein to the T protein.

Subcellular Location:
Mitochondrion.

DISEASE:
Defects in GCSH are a cause of non-ketotic hyperglycinemia (NKH) [MIM:605899]; also known as glycine encephalopathy (GCE). NKH is an autosomal recessive disease characterized by accumulation of a large amount of glycine in body fluid and by severe neurological symptoms.

Similarity:
Belongs to the gcvH family.
Contains 1 lipoyl-binding domain.

Database links:
UniProtKB/Swiss-Prot: P23434.2

Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.ggggww.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 久久久www | 中文字幕12页 | 天天躁日日躁狠狠躁日日躁 | 亚洲精品18日本一区久久 | 中文字幕精品一二三四五六七八 | 潘金莲一级淫片aaa 欧美综合二区 | 国产在线观看免费av | 簧片免费网站 | 成人国产精品久久久春色 | AV剧情麻豆映画国产在线观看 | 在线观看免费视频亚洲 | 巜被社长侵犯的人2中文在线 | 丰满少妇三级全黄 | 色视频在线观看网站 | 区一区二在线 | 永久中文字幕免费视频网站 | 中文字幕无码精品亚洲资源网久久 | 四虎国产在线观看 | 在线涩涩免费观看国产精品 | 精品视频免费久久久看 | 亚洲精品午夜一区人人爽 | 亚洲AV无码一区二区三区系列 | 波多野结衣乳巨码无在线播放 | 欧美精品v国产精品v日韩精品 | 521香蕉| 玖玖精品一区 | 国产在线高清视频无码不卡互動交流 | 欧美黄色片网站 | 日本线在线 | 求一个男人都懂得www | 久久免费视频9 | 又粗又黄又猛又爽大片免费 | 国产亚洲美女精品久久久久 | 亚洲综合网站久久久 | 中文字幕精品久久一区二区三区 | 久久精品视频18 | 久热中文字幕 | 99av海角社区| 7777精品伊久久久大香线蕉 | 91大神免费观看 | 亚洲国产精品成人综合色 |