超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
精品韩国三级在线观看视频,色婷婷久久久久swag精品,亚洲资源在线观看
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-Iduronate 2 sulfatase/Gold Conjugated antibody (bs-15543R-Gold)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul(10nm  15nm  35nm
100ul/2980.00元
大包裝/詢價
產品編號 bs-15543R-Gold
英文名稱 Rabbit Anti-Iduronate 2 sulfatase/Gold Conjugated antibody
中文名稱 膠體金標記的艾杜糖-2-硫酸酯酶抗體
別    名 Alpha L iduronate sulfate sulfatase; Alpha-L-iduronate sulfate sulfatase; AW214631; Ids; IDS_HUMAN; Iduronate 2 sulfatase 14 kDa chain; Iduronate 2 sulfatase 42 kDa chain; Iduronate 2 sulfatase; Iduronate 2-sulfatase 14 kDa chain; Iduronate sulfatase; Idursulfase; MPS2; RP23-29M4.1; SIDS.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul(10nm  15nm  35nm
研究領域 細胞生物  免疫學  細胞類型標志物  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 Human,  (predicted: Mouse, Rat, Dog, Cow, Sheep, )
產品應用 IEM=1:20-200 ICA=1:20-200 ChIP=1:20-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 47kDa
性    狀 Lyophilized or Liquid
濃    度 0.4mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human Iduronate 2 sulfatase
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.02M TBS(pH8.2) with 1% BSA, 0.03% Proclin300.
保存條件 Store at 2-8 oC for 3-6 months. Avoid repeated freeze/thaw cycles.
產品介紹 background:
The protein encoded by this gene belongs to the sulfatase family, is localized to the lysosome, and is involved in lysosomal degradation of heparan sulfate and dermatan sulfate. Mutations in this gene are associated with the X-linked lysosomal storage disease, mucopolysaccharidosis type II, also known as Hunter syndrome. Alternatively spliced transcript variants have been described for this gene. [provided by RefSeq, Aug 2013]

Function:
Required for the lysosomal degradation of heparan sulfate and dermatan sulfate.

Subunit:
Liver iduronate 2-sulfatase is composed of two major forms (A and B) which contain both a 42 kDa and a 14 kDa polypeptides.

Subcellular Location:
Lysosome.

Tissue Specificity:
Liver, kidney, lung, and placenta.

Post-translational modifications:
The conversion to 3-oxoalanine (also known as C-formylglycine, FGly), of a serine or cysteine residue in prokaryotes and of a cysteine residue in eukaryotes, is critical for catalytic activity (By similarity).

DISEASE:
Mucopolysaccharidosis 2 (MPS2) [MIM:309900]: An X-linked lysosomal storage disease characterized by intracellular accumulation of heparan sulfate and dermatan sulfate and their excretion in urine. Most children with MPS2 have a severe form with early somatic abnormalities including skeletal deformities, hepatosplenomegaly, and progressive cardiopulmonary deterioration. A prominent feature is neurological damage that presents as developmental delay and hyperactivity but progresses to mental retardation and dementia. They die before 15 years of age, usually as a result of obstructive airway disease or cardiac failure. In contrast, those with a mild form of MPS2 may survive into adulthood, with attenuated somatic complications and often without mental retardation. Note=The disease is caused by mutations affecting the gene represented in this entry.

Similarity:
Belongs to the sulfatase family.

Database links:

Entrez Gene: 3423 Human

Omim: 309900 Human

SwissProt: P22304 Human

Unigene: 460960 Human



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.ggggww.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 国产精品久久久久四虎 | 蜜臀亚洲AV无码之国产精品 | 精品久久久一二三区 | 阳茎进去女人阳道视频特黄 | 日韩美女毛片 | 国产亚洲日本精品无码 | 亚洲vs天堂 | 黄色片一级毛片 | 国产亚洲一区二区视频 | 一区二区三区免费视频网站 | 成人无码A片一区二区三区免费看 | 中国一级毛片免费视频 | 亚洲宅男天堂 | 爆乳肉体大杂交soe646在线观看 | 2021在线精品自偷自拍无码 | 亚洲综合天堂婷婷五月 | 日本免费高清一区二区 | 6699久久久久久久77777'7 亚洲日韩中文第一精品 | 国产成人精品999在线观看 | 911日本亚洲精品 | 国产v日韩v欧美v在线观看 | 日韩www在线 | 久久久久国产一区二区三区不卡 | 男生操女生视频免费看 | 老司机亚洲精品影院无码 | 国产第五页 | 国产伦理一区 | 熟妇的奶头又大又长奶水视频 | 草久久精品 | 影音先锋男人AV鲁色资源网 | 亚洲最大的av网站 | 国产美女一级做受老师 | 精品小视频在线 | 精品久久久久久久毛片微露脸 | 91成人在线免费 | 一本大道五月香蕉 | 成人一级片在线免费观看 | 91亚洲国产成人精品性色 | 国产真实野战在线视频 | 国产超碰人人做人人爱 | 亚洲成a人片在线不卡一二三区 |