超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
无码一区二区波多野结衣播放搜索,古装三级在线观看,日本久久国产
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-COLQ/BF647 Conjugated antibody (bs-10932R-BF647)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-10932R-BF647
英文名稱 Rabbit Anti-COLQ/BF647 Conjugated antibody
中文名稱 BF647標記的乙酰膽堿酯酶相關膠原蛋白多肽抗體
別    名 Acetylcholinesterase-associated collagen; AChE Q subunit; asymmetric acetylcholinesterase; Collagen-like tail subunit (single strand of homotrimer) of asymmetric acetylcholinesterase; Colq; COLQ_HUMAN; EAD; OTTHUMP00000209566; OTTHUMP00000209567; single strand of homotrimeric collagen-like tail subunit of asymmetric acetylcholinesterase.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 神經生物學  信號轉導  細胞骨架  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應
產品應用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 45kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human COLQ
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
This gene encodes the subunit of a collagen-like molecule associated with acetylcholinesterase in skeletal muscle. Each molecule is composed of three identical subunits. Each subunit contains a proline-rich attachment domain (PRAD) that binds an acetylcholinesterase tetramer to anchor the catalytic subunit of the enzyme to the basal lamina. Mutations in this gene are associated with endplate acetylcholinesterase deficiency. Multiple transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jul 2008]

Function:
Anchors the catalytic subunits of asymmetric AChE to the synaptic basal lamina.

Subcellular Location:
Cell junction; synapse.

Tissue Specificity:
Found at the end plate of skeletal muscle.

Post-translational modifications:
The triple-helical tail is stabilized by disulfide bonds at each end.

DISEASE:
Defects in COLQ are the cause of congenital myasthenic syndrome Engel type (CMSE) [MIM:603034]; also known as end-plate acetylcholinesterase deficiency or congenital myasthenic syndrome type IC (CMS-IC). CMSE is a rare autosomal recessive congenital myasthenic syndrome characterized by onset during childhood, generalized weakness, abnormal fatigability on exertion, refrectoriness to acetylcholinesterase drugs, decremental electromyographic response and morphological abnormalities of the neuromuscular junctions.

Similarity:
Belongs to the COLQ family.
Contains 2 collagen-like domains.

Database links:

Entrez Gene: 8292 Human

Omim: 603033 Human

SwissProt: Q9Y215 Human

Unigene: 146735 Human



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.ggggww.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 男人的天堂啪啪 | 69av一区 | 成人av视频 | 久久aⅴ人妻少妇嫩草影院 脱了我奶罩亲我奶头好舒服 | www.日本在线观看 | 懂色av一区二区三区观看 | 在线超碰 | 无套内谢少妇毛片免费看 | 欧美亚洲另类丝袜综合网 | 最新中文字幕在线视频 | 人妻无码中文字幕一区二区三区 | 狂猛欧美激情性XXXX大豆行情 | 亚洲无码精品在线观看影院 | 国产一卡三卡四卡无卡精品 | 国产精品成人自拍 | A级毛片高清免费视频在线播放 | 久久精av | 艳母1-6在线播放 | 欧美日韩免费做爰大片人 | 亚洲人和日本人hd | 亚洲AV成人无码一区无广告 | 人妻无码AV天堂二区网站 | 日本高清色本在线www | 国产成人精品久久久一区二区三区 | 欧美中文字幕在线播放 | 亚洲交一区 | 女人体(1963)| 视频二区精品中文字幕 | aaa国产大片 | 天天干在线视频论坛 | 精品欧美激情在线观看 | 欧美人成在线视频 | 国色天香乱码区 | 久草在线视频免赞 | 国产一级二级日本在线 | 久久夜色精品国产噜噜亚洲SV | 被绑在机器上强行高潮的视频 | 中文字幕av三区 | 亚洲乱码国产乱码精品精的特点 | 免费AV网站 | 又黄又爽又色视频 |