超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
人人操,天天干,婷婷久久精品一区二区,欧美一级视频在线观看
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-CHRNG/Cy5.5 Conjugated antibody (bs-19245R-Cy5.5)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-19245R-Cy5.5
英文名稱 Rabbit Anti-CHRNG/Cy5.5 Conjugated antibody
中文名稱 Cy5.5標記的煙堿型乙酰膽堿受體γ抗體
別    名 Acetylcholine receptor muscle gamma subunit; Nicotinic Acetylcholine Receptor gamma; Acetylcholine receptor protein gamma chain precursor; Acetylcholine receptor subunit gamma; ACHG; ACHG_HUMAN; Achr 3; Achr3; ACHRG; ACRG; Cholinergic receptor nicotinic gamma; Cholinergic receptor nicotinic gamma polypeptide; CHRNG; MGC133376.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 細胞生物  神經生物學  細胞膜受體  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 (predicted: Human, Mouse, Rat, Dog, Pig, Cow, Horse, Rabbit, )
產品應用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 55kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human CHRNG
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
The mammalian muscle-type acetylcholine receptor is a transmembrane pentameric glycoprotein with two alpha subunits, one beta, one delta, and one epsilon (in adult skeletal muscle) or gamma (in fetal and denervated muscle) subunit. This gene, which encodes the gamma subunit, is expressed prior to the thirty-third week of gestation in humans. The gamma subunit of the acetylcholine receptor plays a role in neuromuscular organogenesis and ligand binding and disruption of gamma subunit expression prevents the correct localization of the receptor in cell membranes. Mutations in this gene cause Escobar syndrome and a lethal form of multiple pterygium syndrome. Muscle-type acetylcholine receptor is the major antigen in the autoimmune disease myasthenia gravis.[provided by RefSeq, Sep 2009]

Function:
After binding acetylcholine, the AChR responds by an extensive change in conformation that affects all subunits and leads to opening of an ion-conducting channel across the plasma membrane.

Subcellular Location:
Cell junction; synapse; postsynaptic cell membrane. Cell membrane.

DISEASE:
Defects in CHRNG are a cause of multiple pterygium syndrome lethal type (MUPSL) [MIM:253290]. Multiple pterygia are found infrequently in children with arthrogryposis and in fetuses with fetal akinesia syndrome. In lethal multiple pterygium syndrome there is intrauterine growth retardation, multiple pterygia, and flexion contractures causing severe arthrogryposis and fetal akinesia. Subcutaneous edema can be severe, causing fetal hydrops with cystic hygroma and lung hypoplasia. Oligohydramnios and facial anomalies are frequent.
Defects in CHRNG are a cause of multiple pterygium syndrome Escobar variant (MUPSE) [MIM:265000]; also known as nonlethal type multiple pterygium syndrome. Escobar syndrome is a non-lethal form of arthrogryposis multiplex congenita. It is an autosomal recessive condition characterized by excessive webbing (pterygia), congenital contractures (arthrogryposis), and scoliosis. Variable other features include intrauterine death, congenital respiratory distress, short stature, faciocranial dysmorphism, ptosis, low-set ears, arachnodactyly and cryptorchism in males. Congenital contractures are common and may be caused by reduced fetal movements at sensitive times of development. Possible causes of decreased fetal mobility include space constraints such as oligohydramnion, drugs, metabolic conditions or neuromuscular disorders including myasthenia gravis. is a.

Similarity:
Belongs to the ligand-gated ion channel (TC 1.A.9) family.
Acetylcholine receptor (TC 1.A.9.1) subfamily.
Gamma/CHRNG sub-subfamily.

Database links:

Entrez Gene: 1146 Human

Omim: 100730 Human

SwissProt: P07510 Human

Unigene: 248101 Human



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.ggggww.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: av影片免费在线观看 | 国产人碰人摸人爱视频日日 | 无遮挡呻吟娇喘视频免费播放 | 精品久久久久一区二区国产 | 不用播放器的av网站 | 一呦二呦三呦精品网站 | 岳好紧好湿夹太紧了好爽矜持 | 欧美最猛黑人xxxx黑人猛叫黄 | 成人乱淫av日日摸夜夜爽 | 久久人人爽人人爽人人片av高请 | 麻豆私人影院 | 激情内射亚洲一区二区三区爱妻 | 成全视频大全免费观看 | 丰满少妇三级全黄 | 狠狠操在线 | 亚洲精品国偷拍自产在线观看蜜臀 | 人人干夜夜 | 密臀av一区二区 | 永久免费av片在线观看全网站 | 国产香蕉97碰碰久久人人九色 | 尤物av无码色av无码 | 国产精品久久麻豆 | 一级免费播放 | 日韩搞逼| 久视频精品线在线观看 | 亚洲一区二区三区无码久久 | 色欲AV午夜一区二区三区 | 麻豆国产在线播放 | 亚洲伊人久久综合成人网站 | 成人亚洲| 日韩国产欧美在线观看 | 国产成人鲁色资源国产91色综 | 亚洲五月综合缴情在线观看 | 在厨房拨开内裤进入毛片 | 国产精品一区二区久久精品爱涩 | 天啦噜国产精品亚洲精品 | 亚洲成人三级在线观看 | 欧美区一区二 | 九九热精品在线 | 青草啪啪 | 国产高清美女一级a毛片久久w |