超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
www..com18午夜观看,国产爆乳无码视频在线观看,99精品一级欧美片免费播放资讯
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-DNAH11/BF555 Conjugated antibody (bs-14360R-BF555)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-14360R-BF555
英文名稱 Rabbit Anti-DNAH11/BF555 Conjugated antibody
中文名稱 BF555標記的軸絲動力蛋白11抗體
別    名 axonemal; Axonemal beta dynein heavy chain 11; axonemal, heavy polypeptide 11; CILD7; Ciliary dynein heavy chain 11; DNAH11; DNAHBL; DNHBL; DPL11; DYH11_HUMAN; Dynein heavy chain 11; dynein, ciliary, heavy chain 11.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 細胞生物  信號轉導  細胞骨架  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 (predicted: Human, Mouse, Rat, Dog, Pig, Cow, Horse, Rabbit, Sheep, )
產品應用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 521kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human DNAH11
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
This gene encodes a ciliary outer dynein arm protein and is a member of the dynein heavy chain family. It is a microtubule-dependent motor ATPase and has been reported to be involved in the movement of respiratory cilia. Mutations in this gene have been implicated in causing Kartagener Syndrome (a combination of situs inversus totalis and Primary Ciliary Dyskinesia (PCD), also called Immotile Cilia Syndrome 1 (ICS1)) and male sterility. [provided by RefSeq, Mar 2013]

Function:
Force generating protein of respiratory cilia. Produces force towards the minus ends of microtubules. Dynein has ATPase activity; the force-producing power stroke is thought to occur on release of ADP.

Subcellular Location:
Cytoplasm; cytoskeleton; cilium axoneme.

DISEASE:
Defects in DNAH11 are a cause of Kartagener syndrome (KTGS) [MIM:244400]. KTGS is an autosomal recessive disorder characterized by the association of primary ciliary dyskinesia with situs inversus. Clinical features include recurrent respiratory infections, bronchiectasis, infertility, and lateral transposition of the viscera of the thorax and abdomen. The situs inversus is most often total, although it can be partial in some cases (isolated dextrocardia or isolated transposition of abdominal viscera). Defects in DNAH11 are the cause of primary ciliary dyskinesia type 7 (CILD7) [MIM:611884]. CILD is an autosomal recessive disorder characterized by axonemal abnormalities of motile cilia. Respiratory infections leading to chronic inflammation and bronchiectasis are recurrent, due to defects in the respiratory cilia; reduced fertility is often observed in male patients due to abnormalities of sperm tails. Half of the patients exhibit situs inversus, due to dysfunction of monocilia at the embryonic node and randomization of left-right body asymmetry. Primary ciliary dyskinesia associated with situs inversus is referred to as Kartagener syndrome.

Similarity:
Belongs to the dynein heavy chain family.

Database links:

Entrez Gene: 8701 Human

Omim: 603339 Human

SwissProt: Q96DT5 Human

Unigene: 520245 Human



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.ggggww.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 熟睡人妻被讨厌的公侵犯 | 欧美久久久久久久久 | 麻豆免费观看网站 | 真人无码国产作爱免费视频 | 亚洲成年人av | 国产精品原创av片国产日韩 | 成人免费色视频 | 国产成人福利在线一区 | 国产精品视频免费看 | 先锋321夜色资源站 欧美性猛交性大交 | 国产tv一区 | 免费又黄又硬又爽大片 | 男女人xx视频 | 国产精品久久免费视频 | 九九热在线视频免费观看 | 亞洲中文字幕第一 | 少妇扒开双腿让我看个够 | www.九色.com| 色欲天天天综合网 | 亚洲精品无码日韩国产不卡AV | 亚洲综合天堂婷婷五月 | 日本99精品 | 中国黄色片一级 | 久久久国产精华液2024特点 | 男生戳美女两腿中间那个视频 | 蜜臀av网页 | 九九热1 | 国产伦码精品一区二区三区 | wwwxxx日本在线观看 | 日美女视频 | 高清无码中字在线一区二区 | 撕开奶罩疯狂揉吮奶头 | 久久久久亚洲AV成人网址 | 一级高清视频 | 国产精品视频yjizz | 亚洲欧美日韩国产高清在线观看 | 日韩高清免费在线 | 中国久久久久 | 丰满少妇被猛烈进入毛片 | 国产成人精选在线观看不卡 | 国产精品扒开腿做爽爽的视频 |