超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關(guān)注公眾號(hào)           掃碼咨詢技術(shù)支持           掃碼咨詢技術(shù)服務(wù)
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  關(guān)于我們  聯(lián)系我們
亚洲一二三区免费视频,超碰97精品,久久国产精品视频免费看
Rabbit Anti-Fumarylacetoacetate hydrolase/HRP Conjugated antibody (bs-16194R-HRP)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術(shù)支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價(jià)
產(chǎn)品編號(hào) bs-16194R-HRP
英文名稱 Rabbit Anti-Fumarylacetoacetate hydrolase/HRP Conjugated antibody
中文名稱 辣根過氧化物酶標(biāo)記的延胡索酰乙酰乙酸水解酶抗體
別    名 Beta diketonase; FAA; FAAA_HUMAN; FAH; Fumarylacetoacetase; Fumarylacetoacetate; Fumarylacetoacetate hydrolase.  
規(guī)格價(jià)格 100ul/2980元 購買        大包裝/詢價(jià)
說 明 書 100ul  
研究領(lǐng)域 腫瘤  細(xì)胞生物  免疫學(xué)  細(xì)胞骨架  新陳代謝  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應(yīng) (predicted: Human, Mouse, Rat, Pig, )
產(chǎn)品應(yīng)用 WB=1:500-2000 ELISA=1:100-1000 IHC-P=1:50-200 IHC-F=1:50-200 ICC=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 47kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human Fumarylacetoacetate hydrolase
亞    型 IgG
純化方法 affinity purified by Protein A
儲(chǔ) 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
This gene encodes the last enzyme in the tyrosine catabolism pathway. FAH deficiency is associated with Type 1 hereditary tyrosinemia (HT). [provided by RefSeq, Jul 2008]

Function:
Fumarylacetoacetate hydrolase is the last enzyme in the tyrosine catabolism pathway. FAH deficiency is associated with Type 1 hereditary tyrosinemia (HT). This is an autosomal recessive inborn error of metabolism that occurs in both an acute and a chronic form. Clinical characteristics of the acute form include hepatic failure and death in infancy, whereas children with the chronic form have renal tubular dysfunction and hypophosphatemic rickets, progressive liver disease with development of hepatocellular carcinoma. Dietary treatment with restriction of tyrosine and phenylalanine alleviates the rickets, but liver transplantation has so far been the only definite treatment.

Subunit:
Homodimer.

Tissue Specificity:
Mainly expressed in liver and kidney. Lower levels are also detected in many other tissues.

Similarity:
Belongs to the FAH family.

Database links:

Entrez Gene: 2184 Human

Entrez Gene: 14085 Mouse

Entrez Gene: 29383 Rat

Omim: 613871 Human

SwissProt: P16930 Human

SwissProt: P35505 Mouse

SwissProt: P25093 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 www.ggggww.cn 北京博奧森生物技術(shù)有限公司
通過國(guó)際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號(hào): 00124Q34771R2M/1100
通過國(guó)際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號(hào): CQC24QY10047R0M/1100
京ICP備05066980號(hào)-1         京公網(wǎng)安備110107000727號(hào)
主站蜘蛛池模板: 中文字幕亚洲综合 | 亚洲国产AV一区二区三区四区 | 欧美成人综合网站 | 亚洲啊v在线观看 | 水蜜桃在线观看视频 | 成人国产精品久久久春色 | 久久久成人影院 | 五十路六十路老熟妇a片 | 天天激情综合 | 久久久国产打桩机 | 最新韩日剧情片在线免费观看 | 色综合激情无码中文字幕 | 天天干天天做 | 亚洲毛片久久 | 日韩欧美国产综合 | 日本成人片网站 | 噼里啪啦2在线观看免费 | 成人18在线观看 | 91亚洲成a人片在线观看www | 蜜臀99久久精品久久久久小说 | 蜜桃无码AV一区二区 | 狠狠色狠狠色综合日日32 | 亚洲av日韩av无码大全 | 毛片TV网站无套内射TV网站 | 日韩中文字幕一区二区高清99 | 色噜噜色狠狠 | 欧美国产视频一区二区 | 一区二区视屏 | 新婚娇妻系列友人妻 | 国产精品igao视频网网址3d | 中文字幕第三区 | 性一交一乱一色一免费无遮挡 | 精品国产美女 | 七级黄色片 | 蜜臀av性色av | 少妇伦子伦精品无吗在线观看 | 天天草夜夜 | 大肉大捧一进一出好爽视色大师 | 国产亚洲第一区 | 在线播放网址亚洲 | hd国产人妖ts另类视频 |