超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
亚洲观看在线,人与拘一级a毛片,国产成人在线网址
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-Fumarylacetoacetate hydrolase/APC Conjugated antibody (bs-16194R-APC)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-16194R-APC
英文名稱 Rabbit Anti-Fumarylacetoacetate hydrolase/APC Conjugated antibody
中文名稱 APC標記的延胡索酰乙酰乙酸水解酶抗體
別    名 Beta diketonase; FAA; FAAA_HUMAN; FAH; Fumarylacetoacetase; Fumarylacetoacetate; Fumarylacetoacetate hydrolase.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 腫瘤  細胞生物  免疫學  細胞骨架  新陳代謝  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 (predicted: Human, Mouse, Rat, Pig, )
產品應用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 47kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human Fumarylacetoacetate hydrolase
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
This gene encodes the last enzyme in the tyrosine catabolism pathway. FAH deficiency is associated with Type 1 hereditary tyrosinemia (HT). [provided by RefSeq, Jul 2008]

Function:
Fumarylacetoacetate hydrolase is the last enzyme in the tyrosine catabolism pathway. FAH deficiency is associated with Type 1 hereditary tyrosinemia (HT). This is an autosomal recessive inborn error of metabolism that occurs in both an acute and a chronic form. Clinical characteristics of the acute form include hepatic failure and death in infancy, whereas children with the chronic form have renal tubular dysfunction and hypophosphatemic rickets, progressive liver disease with development of hepatocellular carcinoma. Dietary treatment with restriction of tyrosine and phenylalanine alleviates the rickets, but liver transplantation has so far been the only definite treatment.

Subunit:
Homodimer.

Tissue Specificity:
Mainly expressed in liver and kidney. Lower levels are also detected in many other tissues.

Similarity:
Belongs to the FAH family.

Database links:

Entrez Gene: 2184 Human

Entrez Gene: 14085 Mouse

Entrez Gene: 29383 Rat

Omim: 613871 Human

SwissProt: P16930 Human

SwissProt: P35505 Mouse

SwissProt: P25093 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.ggggww.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 国产v日韩v欧美v在线观看 | 少妇中文字幕乱码亚洲影视 | 欧美巨大XXXX做受中文字幕 | 亚洲欧美日韩成人综合一区 | 日韩国产成人无码AV毛片 | 爆乳一区二区三区无码 | 国产成人久久av免费高清密臂 | 在线一区不卡 | 国产又硬又粗进去好爽A片软件 | 国产在线精品一区二区中文 | 国产成人啪精品午夜网站 | xxxxx日本69 | 亚洲精品人成网在线播放影院 | 新版天堂8中文在线最新版官网 | 国产超碰人人模人人爽人人添 | 日本添下边无码视频全过程 | 少妇仑乱A毛片无码 | 性大片性大片免费 | 黄频视频在线观看 | 欧美成人一区二区 | 少妇午夜三级伦理影院播放器 | 天天干视频在线观看 | 新婚娇妻系列友人妻 | 天天干天天弄 | 国产精品亚洲А∨天堂网 | 大陆一级毛片免费看 | 久久亚洲色WWW成人欧美 | 男人的天堂Aⅴ在线无码 | HEYZO无码综合国产精品227 | 三男一女吃奶添下面 | 国产亚洲精品俞拍视频 | 一级毛片黄 | 啊灬啊灬啊灬快灬高潮少妇 | 欧美在线观看19 | 农村妇女高清毛片一级 | 成人做爽爽爽爽免费国产软件 | 艳妇乳肉豪妇荡乳XXX | 国产亚洲精品视觉盛宴 | 亚洲精品二三区 | 亚洲综合无码一区二区加勒此 | 新版天堂8中文在线最新版官网 |