超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關(guān)注公眾號(hào)           掃碼咨詢(xún)技術(shù)支持           掃碼咨詢(xún)技術(shù)服務(wù)
  
客服熱線(xiàn):400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  關(guān)于我們  聯(lián)系我們
黄动漫视频,日本大逼,视频一区二区日韩
Rabbit Anti-Fumarylacetoacetate hydrolase/PE-Cy7 Conjugated antibody (bs-16194R-PE-Cy7)
訂購(gòu)熱線(xiàn):400-901-9800
訂購(gòu)郵箱:sales@bioss.com.cn
訂購(gòu)QQ:  400-901-9800
技術(shù)支持:techsupport@bioss.com.cn
說(shuō) 明 書(shū): 100ul  
100ul/2980.00元
大包裝/詢(xún)價(jià)
產(chǎn)品編號(hào) bs-16194R-PE-Cy7
英文名稱(chēng) Rabbit Anti-Fumarylacetoacetate hydrolase/PE-Cy7 Conjugated antibody
中文名稱(chēng) PE-Cy7標(biāo)記的延胡索酰乙酰乙酸水解酶抗體
別    名 Beta diketonase; FAA; FAAA_HUMAN; FAH; Fumarylacetoacetase; Fumarylacetoacetate; Fumarylacetoacetate hydrolase.  
規(guī)格價(jià)格 100ul/2980元 購(gòu)買(mǎi)        大包裝/詢(xún)價(jià)
說(shuō) 明 書(shū) 100ul  
研究領(lǐng)域 腫瘤  細(xì)胞生物  免疫學(xué)  細(xì)胞骨架  新陳代謝  
抗體來(lái)源 Rabbit
克隆類(lèi)型 Polyclonal
交叉反應(yīng) (predicted: Human, Mouse, Rat, Pig, )
產(chǎn)品應(yīng)用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 47kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human Fumarylacetoacetate hydrolase
亞    型 IgG
純化方法 affinity purified by Protein A
儲(chǔ) 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
This gene encodes the last enzyme in the tyrosine catabolism pathway. FAH deficiency is associated with Type 1 hereditary tyrosinemia (HT). [provided by RefSeq, Jul 2008]

Function:
Fumarylacetoacetate hydrolase is the last enzyme in the tyrosine catabolism pathway. FAH deficiency is associated with Type 1 hereditary tyrosinemia (HT). This is an autosomal recessive inborn error of metabolism that occurs in both an acute and a chronic form. Clinical characteristics of the acute form include hepatic failure and death in infancy, whereas children with the chronic form have renal tubular dysfunction and hypophosphatemic rickets, progressive liver disease with development of hepatocellular carcinoma. Dietary treatment with restriction of tyrosine and phenylalanine alleviates the rickets, but liver transplantation has so far been the only definite treatment.

Subunit:
Homodimer.

Tissue Specificity:
Mainly expressed in liver and kidney. Lower levels are also detected in many other tissues.

Similarity:
Belongs to the FAH family.

Database links:

Entrez Gene: 2184 Human

Entrez Gene: 14085 Mouse

Entrez Gene: 29383 Rat

Omim: 613871 Human

SwissProt: P16930 Human

SwissProt: P35505 Mouse

SwissProt: P25093 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 www.ggggww.cn 北京博奧森生物技術(shù)有限公司
通過(guò)國(guó)際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書(shū)編號(hào): 00124Q34771R2M/1100
通過(guò)國(guó)際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書(shū)編號(hào): CQC24QY10047R0M/1100
京ICP備05066980號(hào)-1         京公網(wǎng)安備110107000727號(hào)
主站蜘蛛池模板: 九色一区 | 国产精品不卡在线播放 | 8mav精品成人 | 夜夜草天天草 | 国产男女做爰猛烈叫床小说 | 国产欧美一区二区三区久久手机版 | 亚洲高清无码在线观看 | 中文字幕日韩精品一区二区 | 久久精品国产成人 | 2020日日夜夜噜噜噜com | 美女黄色一级视频 | 户外露出一区二区三区 | 国产精品嫩草影院一二三区入口 | 国内精拍拍在线视频免费看 | 国产成人啪精品视频免费软件 | 337p日本欧洲亚洲大胆张筱雨 | 毛片在线免费观看网站 | 96精品成人无码A片观看金桔 | 日韩av一二三区 | 久久亚洲综合精品99国产 | 久久久免费在线观看 | 欧美成人A片一区二区不卡 www.日日干 麻豆特级毛片 | 精品中文字幕一区 | 亚洲国产精彩视频 | gav成人网免费免播放器播放 | 又粗又大又黄又硬又爽免费看 | 3ce奇米四色眼影奇米8888 | 偷拍自拍视频在线观看 | 91jq激情 | 又硬又粗进去好爽A片春色视频 | 日本影院一区 | 九七影院97影院理论片久久 | 亚洲狠狠做深爱婷婷影院 | 日本添下边无码视频全过程 | 国产特色特黄的视频免费观看 | 精品二区在线 | 欧美日韩激情一级 | 青青草原综合久久大伊人 | 亚洲综合熟女久久久30p | 婷婷开心深爱五月天播播 | 欧洲影视字幕中文 |