超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
国产午夜福利久久精品,久久夜色精品国产噜噜亚洲SV,色爱综合
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-Tropomyosin 3/FITC Conjugated antibody (bs-17158R-FITC)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-17158R-FITC
英文名稱 Rabbit Anti-Tropomyosin 3/FITC Conjugated antibody
中文名稱 FITC標記的γ-原肌球蛋白/原肌球蛋白3抗體
別    名 Alpha tropomyosin 3; Alpha tropomyosin slow skeletal; CFTD; Cytoskeletal tropomyosin TM30; FLJ41118; gamma TM; Gamma tropomyosin; Gamma-tropomyosin; Heat stable cytoskeletal protein 30 kDa; hscp30; hTM30nm; hTM5; hTMnm; MGC102590; MGC14582; MGC3261; MGC72094; NEM1; OK/SW-cl.5; OTTHUMP00000034019; OTTHUMP00000034171; OTTHUMP00000034172; TM 5; TM-5; TM3; TM30; TM30nm; TM5; Tm5NM; Tpm 5; TPM3; TPM3/NTRK1 FUSION GENE, INCLUDED; TPM3_HUMAN; Tpm5; TPMsk3; TRK; TRK ONCOGENE, INCLUDED; Trop 5; Tropomyosin 3; Tropomyosin 3 gamma; Tropomyosin 5; Tropomyosin alpha 3 chain; Tropomyosin alpha-3 chain; Tropomyosin gamma; Tropomyosin-3; Tropomyosin-5.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 腫瘤  細胞生物  信號轉導  結合蛋白  細胞骨架  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 (predicted: Human, Mouse, Rat, Chicken, Dog, Pig, Cow, Horse, )
產品應用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 33kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human Tropomyosin 3
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
This gene encodes a member of the tropomyosin family of actin-binding proteins. Tropomyosins are dimers of coiled-coil proteins that provide stability to actin filaments and regulate access of other actin-binding proteins. Mutations in this gene result in autosomal dominant nemaline myopathy and other muscle disorders. This locus is involved in translocations with other loci, including anaplastic lymphoma receptor tyrosine kinase (ALK) and neurotrophic tyrosine kinase receptor type 1 (NTRK1), which result in the formation of fusion proteins that act as oncogenes. There are numerous pseudogenes for this gene on different chromosomes. Alternative splicing results in multiple transcript variants. [provided by RefSeq, May 2013]

Function:
Binds to actin filaments in muscle and non-muscle cells. Plays a central role, in association with the troponin complex, in the calcium dependent regulation of vertebrate striated muscle contraction. Smooth muscle contraction is regulated by interaction with caldesmon. In non-muscle cells is implicated in stabilizing cytoskeleton actin filaments.

Subcellular Location:
Cytoplasm > cytoskeleton.

DISEASE:
Defects in TPM3 are the cause of nemaline myopathy type 1 (NEM1) [MIM:609284]. A form of nemaline myopathy with autosomal dominant or recessive inheritance. Nemaline myopathies are muscular disorders characterized by muscle weakness of varying severity and onset, and abnormal thread-or rod-like structures in muscle fibers on histologic examination. Autosomal dominant nemaline myopathy type 1 is characterized by a moderate phenotype with onset between birth and early second decade of life. Weakness is diffuse and symmetric with slow progression often with need for a wheelchair in adulthood. The autosomal recessive form has onset at birth with moderate-to-severe hypotonia and diffuse weakness. In the most severe cases, death can occur before 2 years. Less severe cases have delayed major motor milestones, and these patients may walk, but often need a wheelchair before 10 years. Defects in TPM3 are a cause of thyroid papillary carcinoma (TPC) [MIM:188550]. TPC is a common tumor of the thyroid that typically arises as an irregular, solid or cystic mass from otherwise normal thyroid tissue. Papillary carcinomas are malignant neoplasm characterized by the formation of numerous, irregular, finger-like projections of fibrous stroma that is covered with a surface layer of neoplastic epithelial cells. Note=A chromosomal aberration involving TPM3 is found in thyroid papillary carcinomas. A rearrangement with NTRK1 generates the TRK fusion transcript by fusing the amino end of isoform 2 of TPM3 to the 3'-end of NTRK1.

Similarity:
Belongs to the tropomyosin family.

Database links:

Entrez Gene: 7170 Human

Entrez Gene: 59069 Mouse

Entrez Gene: 414388 Pig

Entrez Gene: 117557 Rat

Omim: 191030 Human

SwissProt: P06753 Human

SwissProt: P21107 Mouse

SwissProt: A1XQV4 Pig

SwissProt: Q63610 Rat

Unigene: 535581 Human

Unigene: 644306 Human

Unigene: 654421 Human

Unigene: 240839 Mouse

Unigene: 421791 Mouse

Unigene: 37575 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.ggggww.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 最新韩日剧情片在线免费观看 | 亚洲热妇无码播放aV另类 | 久久国产午夜精品理论片34页 | 超碰成人久久 | 久久精品爱爱视频 | 久久青草网站 | 久章草在线精品视频免费观看 | 铠甲勇士第一部52集全 | A级毛片高清免费视频在线播放 | 亚洲一区二区三区AV天堂 | 夜夜操网| 色香欲综合成人免费视频 | 国产亚洲精品无码在线观看 | 一区二区精品在线观看 | 亚州精品av久久久久久久影院 | 久久精品国产久精国产爱 | 久久免费看少妇高潮a片特黄 | 看免费一级片 | 欧美视频二区欧美影视 | 少妇SPA推油被扣高潮在线观看 | 大陆极品少妇内射aaaaa | 美女日p | 国产成人精品久久亚洲高清不卡p | 日本熟妇XXXⅩ50岁 | 久久国产免费视频 | 久热中文在线 | 欧美国产视频一区二区 | 港台一级毛片 | 色欲综合久久躁天天躁蜜桃 | 国产一区二区三区乱码在线观看 | 欧美成人aaa级毛片在线视频 | 日本不卡一区二区三区在线 | 粉嫩av一区二区三区入口 | 开妇小嫩苞调教HHH嗯啊MTV | 一级无遮挡真人毛片黄色视频 | 国产高清不卡一区二区三区 | 国产精品亚洲一区二区三区正片 | 137大胆人体在线观看 | 97精品国产97久久久久久久久久久久 | 国产福利91 | 逼逼影视 |