超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
岛国视频免费在线观看,一区二区黄色,国产亚洲精品一区二区
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-HPS2/Cy5.5 Conjugated antibody (bs-17380R-Cy5.5)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-17380R-Cy5.5
英文名稱 Rabbit Anti-HPS2/Cy5.5 Conjugated antibody
中文名稱 Cy5.5標記的HPS2蛋白抗體
別    名 Adapter related protein complex 3 beta 1 subunit; Adapter-related protein complex 3 subunit beta-1; Adaptor protein complex AP-3 subunit beta-1; Adaptor protein complex AP3 beta1 subunit; ADTB3; ADTB3A; AP-3 complex subunit beta-1; AP3 complex beta1 subunit; AP3B1; AP3B1_HUMAN; Beta-3A-adaptin; Beta3A adaptin; Clathrin assembly protein complex 3 beta 1 large chain; Clathrin assembly protein complex 3 beta-1 large chain; HPS; PE.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 細胞生物  免疫學  信號轉導  轉運蛋白  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 Human, Mouse,  (predicted: Rat, Dog, Pig, Cow, Horse, Rabbit, Sheep, Cat,  Xenopus laevis)
產品應用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 121kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human HPS2
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
This gene encodes a protein that may play a role in organelle biogenesis associated with melanosomes, platelet dense granules, and lysosomes. The encoded protein is part of the heterotetrameric AP-3 protein complex which interacts with the scaffolding protein clathrin. Mutations in this gene are associated with Hermansky-Pudlak syndrome type 2. Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Nov 2012]

Function:
Subunit of non-clathrin- and clathrin-associated adaptor protein complex 3 that plays a role in protein sorting in the late-Golgi/trans-Golgi network (TGN) and/or endosomes. The AP complexes mediate both the recruitment of clathrin to membranes and the recognition of sorting signals within the cytosolic tails of transmembrane cargo molecules. AP-3 appears to be involved in the sorting of a subset of transmembrane proteins targeted to lysosomes and lysosome-related organelles.

Subcellular Location:
Golgi apparatus. Cytoplasmic vesicle > clathrin-coated vesicle membrane. Golgi apparatus. Component of the coat surrounding the cytoplasmic face of coated vesicles located at the Golgi complex.

Tissue Specificity:
Ubiquitously expressed.

Post-translational modifications:
Phosphorylated on serine residues.

DISEASE:
Defects in AP3B1 are the cause of Hermansky-Pudlak syndrome type 2 (HPS2) [MIM:608233]. Hermansky-Pudlak syndrome (HPS) is a genetically heterogeneous, rare, autosomal recessive disorder characterized by oculocutaneous albinism, bleeding due to platelet storage pool deficiency, and lysosomal storage defects. This syndrome results from defects of diverse cytoplasmic organelles including melanosomes, platelet dense granules and lysosomes. Ceroid storage in the lungs is associated with pulmonary fibrosis, a common cause of premature death in individuals with HPS. HPS2 differs from the other forms of HPS in that it includes immunodeficiency in its phenotype and patients with HPS2 have an increased susceptibility to infections.

Similarity:
Belongs to the adaptor complexes large subunit family.

Database links:

Entrez Gene: 767602 Cow

Entrez Gene: 403459 Dog

Entrez Gene: 8546 Human

Entrez Gene: 11774 Mouse

Entrez Gene: 100049670 Pig

Entrez Gene: 443724 Xenopus laevis

Omim: 603401 Human

SwissProt: Q32PG1 Cow

SwissProt: Q7YRF1 Dog

SwissProt: O00203 Human

SwissProt: Q9Z1T1 Mouse

Unigene: 532091 Human

Unigene: 21185 Mouse



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.ggggww.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 海角国精产品一区一区三区糖心 | 亚洲∧V久久久无码精品 | 无码国产精品免费看 | 亚洲成人手机在线观看 | 欧美肥胖老太bbw | 久久超碰极品视觉盛宴 | 国产精品狼人色视频一区 | 7777在线视频| 欧美成人乱码一二三四区 | 久久精品在线免费视频 | 成人在线欧美 | 日韩一级片免费视频 | 成人免费视频视频 | 久久综合中文字幕一区二区三区 | 欧美伦理大片 | 国产农村熟妇videos | 在线日一区 | 国产ww久久久久久久久久 | 国产精品久久久久久男贼秘图 | 国产AV尤物一区二区三区 | 五月激情网站 | 久久久久久成人 | 影音先锋在线中文字幕 | www.哥也色.com | 强伦人妻一区二区三区视频18 | 亚洲国产一区精品 | 亚洲天堂中文字幕在线观看 | 日本高清VA在线播放 | 国产精品人妻无码久久久苍井空 | 日韩卡一卡二无线乱码新区仙踪林 | 日韩视频精品在线 | 久久精品成人无码观看56 | 99久久久久国产精品免费 | 亚洲国产精品久久久久婷婷老年 | 一级片视频免费 | 国产精品热视频 | 成全动漫在线观看免费观看 | 亚洲国产成人久久一区www妖精 | 久草在线免费福利资源 | 不卡的在线视频 | xxxx中国一级片 |