超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
国产精品社区在线观看,开心婷婷中文字幕,久久夜色精品国产噜噜亚洲AV
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-COX10/Cy7 Conjugated antibody (bs-23098R-Cy7)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-23098R-Cy7
英文名稱 Rabbit Anti-COX10/Cy7 Conjugated antibody
中文名稱 Cy7標記的細胞色素c氧化酶10抗體
別    名 Heme A farnesyltransferase; Heme O synthase; OTTMUSP00000006085; Protoheme IX farnesyltransferase, mitochondrial precursor; RP23-78H18.1; 2410004F01Rik; AU042636; Cytochrome c oxidase assembly protein; Cytochrome c oxidase subunit X; COX10_HUMAN; Protoheme IX farnesyltransferase, mitochondrial; Heme O synthase.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 腫瘤  細胞生物  信號轉導  通道蛋白  新陳代謝  線粒體  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 Human, Mouse,  (predicted: Rat, )
產品應用
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 49kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human COX10
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
Cytochrome c oxidase (COX), the terminal component of the mitochondrial respiratory chain, catalyzes the electron transfer from reduced cytochrome c to oxygen. This component is a heteromeric complex consisting of 3 catalytic subunits encoded by mitochondrial genes and multiple structural subunits encoded by nuclear genes. The mitochondrially-encoded subunits function in electron transfer, and the nuclear-encoded subunits may function in the regulation and assembly of the complex. This nuclear gene encodes heme A:farnesyltransferase, which is not a structural subunit but required for the expression of functional COX and functions in the maturation of the heme A prosthetic group of COX. This protein is predicted to contain 7-9 transmembrane domains localized in the mitochondrial inner membrane. A gene mutation, which results in the substitution of a lysine for an asparagine (N204K), is identified to be responsible for cytochrome c oxidase deficiency. In addition, this gene is disrupted in patients with CMT1A (Charcot-Marie-Tooth type 1A) duplication and with HNPP (hereditary neuropathy with liability to pressure palsies) deletion. [provided by RefSeq, Jul 2008]

Function:
Converts protoheme IX and farnesyl diphosphate to heme O.

Subcellular Location:
Mitochondrion membrane; Multi-pass membrane protein.

DISEASE:
Mitochondrial complex IV deficiency (MT-C4D) [MIM:220110]: A disorder of the mitochondrial respiratory chain with heterogeneous clinical manifestations, ranging from isolated myopathy to severe multisystem disease affecting several tissues and organs. Features include hypertrophic cardiomyopathy, hepatomegaly and liver dysfunction, hypotonia, muscle weakness, exercise intolerance, developmental delay, delayed motor development and mental retardation. Some affected individuals manifest a fatal hypertrophic cardiomyopathy resulting in neonatal death. A subset of patients manifest Leigh syndrome. Note=The disease is caused by mutations affecting the gene represented in this entry.
Leigh syndrome (LS) [MIM:256000]: An early-onset progressive neurodegenerative disorder characterized by the presence of focal, bilateral lesions in one or more areas of the central nervous system including the brainstem, thalamus, basal ganglia, cerebellum and spinal cord. Clinical features depend on which areas of the central nervous system are involved and include subacute onset of psychomotor retardation, hypotonia, ataxia, weakness, vision loss, eye movement abnormalities, seizures, and dysphagia. Note=The disease is caused by mutations affecting the gene represented in this entry.

Similarity:
Belongs to the UbiA prenyltransferase family.

Database links:

Entrez Gene: 417329 Chicken

Entrez Gene: 511440 Cow

Entrez Gene: 1352 Human

Entrez Gene: 70383 Mouse

Entrez Gene: 363617 Rat

Entrez Gene: 553384 Zebrafish

Omim: 602125 Human

SwissProt: Q12887 Human

SwissProt: Q8CFY5 Mouse

Unigene: 462278 Human

Unigene: 340211 Mouse



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.ggggww.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 亚洲美女视频一区二区 | 日韩av一级片 | 国产精品亚洲аv久久亚瑟桃花 | 亚洲欧美成人在线 | 成年人av在线免费观看 | 岛国无码av不卡一区二区 | 日本高清一区二区视频 | 农村少妇好紧水多视频 | 99色免费视频 | 日本强伦片中文字幕免费看 | 国产毛片毛多水多的特级毛片 | 久久夜色精品国产www | 国产高清在线免费视频 | 搡少妇在线视频少妇干活了 | 超级碰碰青草免费视频 | 一级片在线免费播放 | 欧美13一14娇小性 | 又粗又大又黄又硬又爽免费看 | 最新国自产拍av | 色人阁色五月 | 377人体裸体露私图片 | 看日本黄色一级高清网站 | 99久久久久国产精品免费 | 国产成人亚洲精品影院 | 永夜星河短剧免费观看 | 97夜夜澡人人爽人人 | 国产精品热视频 | 欧美一区日本一区韩国一区 | 日本打屁股调教免费网站 | 国产和日产视频免费观看 | 久热RE这里精品视频在线6 | 精品久久久久久中文字幕2017 | 老司机午夜在线视频 | 小妖精又紧又湿高潮H视频69 | 在线超碰 | 91欧美视频在线 | www.久久草.com | 久久av每日更新免费观看 | 午夜视频在线观 | 欧美色视频在线观看 | 狠狠躁夜夜躁人人爽天天开心婷婷 |