超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
美景之屋3在线观看,久久久久久久国产精品免费播放,中文字幕在线观看日
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-COX10/PE-Cy3 Conjugated antibody (bs-23098R-PE-Cy3)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-23098R-PE-Cy3
英文名稱 Rabbit Anti-COX10/PE-Cy3 Conjugated antibody
中文名稱 PE-Cy3標記的細胞色素c氧化酶10抗體
別    名 Heme A farnesyltransferase; Heme O synthase; OTTMUSP00000006085; Protoheme IX farnesyltransferase, mitochondrial precursor; RP23-78H18.1; 2410004F01Rik; AU042636; Cytochrome c oxidase assembly protein; Cytochrome c oxidase subunit X; COX10_HUMAN; Protoheme IX farnesyltransferase, mitochondrial; Heme O synthase.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 腫瘤  細胞生物  信號轉導  通道蛋白  新陳代謝  線粒體  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 Human, Mouse,  (predicted: Rat, )
產品應用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 49kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human COX10
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
Cytochrome c oxidase (COX), the terminal component of the mitochondrial respiratory chain, catalyzes the electron transfer from reduced cytochrome c to oxygen. This component is a heteromeric complex consisting of 3 catalytic subunits encoded by mitochondrial genes and multiple structural subunits encoded by nuclear genes. The mitochondrially-encoded subunits function in electron transfer, and the nuclear-encoded subunits may function in the regulation and assembly of the complex. This nuclear gene encodes heme A:farnesyltransferase, which is not a structural subunit but required for the expression of functional COX and functions in the maturation of the heme A prosthetic group of COX. This protein is predicted to contain 7-9 transmembrane domains localized in the mitochondrial inner membrane. A gene mutation, which results in the substitution of a lysine for an asparagine (N204K), is identified to be responsible for cytochrome c oxidase deficiency. In addition, this gene is disrupted in patients with CMT1A (Charcot-Marie-Tooth type 1A) duplication and with HNPP (hereditary neuropathy with liability to pressure palsies) deletion. [provided by RefSeq, Jul 2008]

Function:
Converts protoheme IX and farnesyl diphosphate to heme O.

Subcellular Location:
Mitochondrion membrane; Multi-pass membrane protein.

DISEASE:
Mitochondrial complex IV deficiency (MT-C4D) [MIM:220110]: A disorder of the mitochondrial respiratory chain with heterogeneous clinical manifestations, ranging from isolated myopathy to severe multisystem disease affecting several tissues and organs. Features include hypertrophic cardiomyopathy, hepatomegaly and liver dysfunction, hypotonia, muscle weakness, exercise intolerance, developmental delay, delayed motor development and mental retardation. Some affected individuals manifest a fatal hypertrophic cardiomyopathy resulting in neonatal death. A subset of patients manifest Leigh syndrome. Note=The disease is caused by mutations affecting the gene represented in this entry.
Leigh syndrome (LS) [MIM:256000]: An early-onset progressive neurodegenerative disorder characterized by the presence of focal, bilateral lesions in one or more areas of the central nervous system including the brainstem, thalamus, basal ganglia, cerebellum and spinal cord. Clinical features depend on which areas of the central nervous system are involved and include subacute onset of psychomotor retardation, hypotonia, ataxia, weakness, vision loss, eye movement abnormalities, seizures, and dysphagia. Note=The disease is caused by mutations affecting the gene represented in this entry.

Similarity:
Belongs to the UbiA prenyltransferase family.

Database links:

Entrez Gene: 417329 Chicken

Entrez Gene: 511440 Cow

Entrez Gene: 1352 Human

Entrez Gene: 70383 Mouse

Entrez Gene: 363617 Rat

Entrez Gene: 553384 Zebrafish

Omim: 602125 Human

SwissProt: Q12887 Human

SwissProt: Q8CFY5 Mouse

Unigene: 462278 Human

Unigene: 340211 Mouse



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.ggggww.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 精品人妻无码一区二区三区手机板 | 国产一级片免费 | 欧美性猛交xxxx乱大交久久 | 亚洲一区综合 | 中文字幕精品久久一区二区三区 | 91一区二区| 久热RE这里精品视频在线6 | 国产免费黄色网址 | 色999久久久精品人人澡69 | 久久久99精品 | 特级毛片在线 | 久久久久综合 | 亚洲国产精品久久久久婷婷图片 | 亚洲AV永久无码精品放毛片 | 国产亚洲视频免费在线儿观看 | 一级特黄色大片 | chinese国产高清av内谢 | 亚洲伊人久久精品酒店 | 噼里啪啦在线视频免费观看 | 初高中洗澡福利网站 | 在线观看免费AV无码不卡 | 性色av蜜臀av高清久久苏然 | 国产精品久久久aaa 欧美乱强伦XXXXX | 国产不卡一区二区在线观看 | 97无码免费人妻超级碰碰碰碰 | 国产制服日韩丝袜86页 | 日韩免费区 | 观看免费av | 成片人免费观看一级A片 | 亚洲欧美日韩在线一区二区三区 | 成人片黄网站A片免费 | 国产精品久久久久久久综合 | 48久久国产精品性色aⅴ人妻 | 日韩精品中文字幕无码专区 | 欧美一页 | 欧美一区日本一区韩国一区 | 色爱区综合 | 免费无套内谢少妇毛片A片软 | 7194中文乱码一二三四芒果 | 久久精品国产一区 | 欧美性生活视频网站 |