超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關(guān)注公眾號           掃碼咨詢技術(shù)支持           掃碼咨詢技術(shù)服務(wù)
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  關(guān)于我們  聯(lián)系我們
永久免费观看国产裸体美女,日本理伦片午夜理伦片,蜜臀av午夜一区二区三区gif
Rabbit Anti-COX10/PE-Cy5.5 Conjugated antibody (bs-23098R-PE-Cy5.5)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術(shù)支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產(chǎn)品編號 bs-23098R-PE-Cy5.5
英文名稱 Rabbit Anti-COX10/PE-Cy5.5 Conjugated antibody
中文名稱 PE-Cy5.5標(biāo)記的細(xì)胞色素c氧化酶10抗體
別    名 Heme A farnesyltransferase; Heme O synthase; OTTMUSP00000006085; Protoheme IX farnesyltransferase, mitochondrial precursor; RP23-78H18.1; 2410004F01Rik; AU042636; Cytochrome c oxidase assembly protein; Cytochrome c oxidase subunit X; COX10_HUMAN; Protoheme IX farnesyltransferase, mitochondrial; Heme O synthase.  
規(guī)格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領(lǐng)域 腫瘤  細(xì)胞生物  信號轉(zhuǎn)導(dǎo)  通道蛋白  新陳代謝  線粒體  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應(yīng) Human, Mouse,  (predicted: Rat, )
產(chǎn)品應(yīng)用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 49kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human COX10
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
Cytochrome c oxidase (COX), the terminal component of the mitochondrial respiratory chain, catalyzes the electron transfer from reduced cytochrome c to oxygen. This component is a heteromeric complex consisting of 3 catalytic subunits encoded by mitochondrial genes and multiple structural subunits encoded by nuclear genes. The mitochondrially-encoded subunits function in electron transfer, and the nuclear-encoded subunits may function in the regulation and assembly of the complex. This nuclear gene encodes heme A:farnesyltransferase, which is not a structural subunit but required for the expression of functional COX and functions in the maturation of the heme A prosthetic group of COX. This protein is predicted to contain 7-9 transmembrane domains localized in the mitochondrial inner membrane. A gene mutation, which results in the substitution of a lysine for an asparagine (N204K), is identified to be responsible for cytochrome c oxidase deficiency. In addition, this gene is disrupted in patients with CMT1A (Charcot-Marie-Tooth type 1A) duplication and with HNPP (hereditary neuropathy with liability to pressure palsies) deletion. [provided by RefSeq, Jul 2008]

Function:
Converts protoheme IX and farnesyl diphosphate to heme O.

Subcellular Location:
Mitochondrion membrane; Multi-pass membrane protein.

DISEASE:
Mitochondrial complex IV deficiency (MT-C4D) [MIM:220110]: A disorder of the mitochondrial respiratory chain with heterogeneous clinical manifestations, ranging from isolated myopathy to severe multisystem disease affecting several tissues and organs. Features include hypertrophic cardiomyopathy, hepatomegaly and liver dysfunction, hypotonia, muscle weakness, exercise intolerance, developmental delay, delayed motor development and mental retardation. Some affected individuals manifest a fatal hypertrophic cardiomyopathy resulting in neonatal death. A subset of patients manifest Leigh syndrome. Note=The disease is caused by mutations affecting the gene represented in this entry.
Leigh syndrome (LS) [MIM:256000]: An early-onset progressive neurodegenerative disorder characterized by the presence of focal, bilateral lesions in one or more areas of the central nervous system including the brainstem, thalamus, basal ganglia, cerebellum and spinal cord. Clinical features depend on which areas of the central nervous system are involved and include subacute onset of psychomotor retardation, hypotonia, ataxia, weakness, vision loss, eye movement abnormalities, seizures, and dysphagia. Note=The disease is caused by mutations affecting the gene represented in this entry.

Similarity:
Belongs to the UbiA prenyltransferase family.

Database links:

Entrez Gene: 417329 Chicken

Entrez Gene: 511440 Cow

Entrez Gene: 1352 Human

Entrez Gene: 70383 Mouse

Entrez Gene: 363617 Rat

Entrez Gene: 553384 Zebrafish

Omim: 602125 Human

SwissProt: Q12887 Human

SwissProt: Q8CFY5 Mouse

Unigene: 462278 Human

Unigene: 340211 Mouse



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 www.ggggww.cn 北京博奧森生物技術(shù)有限公司
通過國際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網(wǎng)安備110107000727號
主站蜘蛛池模板: 午夜免费1000 | 特级毛片在线免费观看 | 91插视频 | 欧美老人巨大xxxx做受 | 欧美美女一区二区 | 日韩av一区二区三区美女毛片 | 久久久久久九九九 | 久久99精品国产自在现线小黄鸭 | 欧美最大胆的西西人体44 | 国产精品久久777777毛茸茸 | 黄色成年人国语版在线观看 | 日本无码一区二区三区在线观看 | 歪歪羞羞嘿咻汗汗av禁漫天堂 | 午夜福利啪啪体验区 | 国产精品久久久999 色婷婷av一区二区三区小说 | 浮生影院大全免费观看 | 91精品免费在线观看 | 日日摸夜夜添夜夜添牛牛 | 日本成a人片在线观看日本 久久婷婷五月综合色国产免费观看 | 日韩精品人妻系列无码专区免费 | 国产精品狼人久久久久影院 | 国产成人福利在线一区 | 国产精品一区二区三区四区五区 | 国产精品美女一区二区 | 延禧攻略免费在线观看 | 国产人成无码视频在线1000 | 国产高潮流白浆免费视频 | 少妇人妻好深太紧了 | 亚洲AV永久无码精品主页 | 精品欧美激情在线观看 | 国产成人免费av一区二区午夜 | 不卡一不卡二不卡三 | 成人性视频免费看的鲁片 | 女人一级一片30分 | 亚洲日韩精品射精日 | 亚洲视频一区二 | 奶头好大揉着好爽GIF动态图 | 成年女人18级毛片毛片免费 | 区二区欧美性插b在线视频网站 | 无码人妻一区二区三区免费视频 | 亚洲欧美成人一区二区 |