超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
国产成人精品人人2020视频,国产精品亚欧美一区二区,免费人成又黄又爽的视频
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-PLOD3/PE-Cy5 Conjugated antibody (bs-12732R-PE-Cy5)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-12732R-PE-Cy5
英文名稱 Rabbit Anti-PLOD3/PE-Cy5 Conjugated antibody
中文名稱 PE-Cy5標記的賴氨酸羥化酶3抗體
別    名 2-oxoglutarate 5-dioxygenase 3; bone protein I; BP-I; LH3; Lysine hydroxylase 3; Lysyl hydroxylase 3; Plod3; PLOD3_HUMAN; Procollagen lysine,2 oxoglutarate 5 dioxygenase 3 precursor; Procollagen-lysine.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 細胞生物  免疫學  細胞膜蛋白  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 Mouse,  (predicted: Human, Rat, Dog, Pig, Cow, Horse, Rabbit, Sheep, )
產品應用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 82kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human PLOD3
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
The protein encoded by this gene is a membrane-bound homodimeric enzyme that is localized to the cisternae of the rough endoplasmic reticulum. The enzyme (cofactors iron and ascorbate) catalyzes the hydroxylation of lysyl residues in collagen-like peptides. The resultant hydroxylysyl groups are attachment sites for carbohydrates in collagen and thus are critical for the stability of intermolecular crosslinks. Some patients with Ehlers-Danlos syndrome type VIB have deficiencies in lysyl hydroxylase activity. [provided by RefSeq, Jul 2008]

Function:
Forms hydroxylysine residues in -Xaa-Lys-Gly- sequences in collagens. These hydroxylysines serve as sites of attachment for carbohydrate units and are essential for the stability of the intermolecular collagen cross-links.

Subcellular Location:
Rough endoplasmic reticulum membrane.

DISEASE:
Defects in PLOD3 are the cause of lysyl hydroxylase 3 deficiency (LH3 deficiency) [MIM:612394]; also known as bone fragility with contractures arterial rupture and deafness. LH3 deficiency is a connective tissue disorder. The syndrome is characterized by congenital malformations severely affecting many tissues and organs and revealing features of several collagen disorders, most of them involving COL2A1 (type II collagen). The findings suggest that the failure of lysyl hydroxylation and hydroxylysyl carbohydrate addition, which affects many collagens, is the molecular basis of this syndrome.

Similarity:
Contains 1 Fe2OG dioxygenase domain.

Database links:

Entrez Gene: 8985 Human

Entrez Gene: 26433 Mouse

Entrez Gene: 288583 Rat

Omim: 603066 Human

SwissProt: O60568 Human

SwissProt: Q9R0E1 Mouse

SwissProt: Q5U367 Rat

Unigene: 153357 Human

Unigene: 251003 Mouse

Unigene: 90152 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.ggggww.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 日本xxxxxxxxx70hd 国内外成人在线视频 | 国产视频第二页 | 无遮无挡爽爽免费视频毛片韩国 | 日韩一级黄色片 | ww好吊妞988gaocom| 欧美精品久久久久久久久老牛影院 | 日韩av一级片 | 99色免费视频 | 84pao国产成人高清在线 | 第一色区 | 青青伊人久久 | 99热3| 成人黄频| 好紧好湿好黄的视频 | 亚洲欧美日韩国产成人一区 | 五月网址 | 精品一区二区视频在线 | 影音先锋男人AV橹橹色 | 在线观看国产精品一区 | 精品黑人一区二区三区久久 | 99爱国产精品 | 久久影院久久 | 国产在线播放精品 | 超鹏97国语| FREEZEFRAME丰满老妇 | 国产国语一级毛片 | 国产jizz18高清视频 | 性色视频 | 中文字幕第三区 | 高清日韩a级毛片精品 | 天天摸夜夜摸爽爽狠狠婷婷97 | 国产网曝门视频在线看 | 一区二区三区 | 新国产三级在线观看播放 | 中文字幕爆乳JULIA女教师 | 亚洲一区二区三区无码久久 | 亚洲精品乱码久久久久久久 | 伊人无码一区二区三区 | 91久久国产综合久久91猫猫 | 亚洲精品无码不卡在线播放 | 99久久国产这里只有精品 |