超碰97自拍_久久99久久98精品免观看软件_在线亚洲一区_九九视频这里只有精品_国产精品一区二区欧美视频_精品国产区一区

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯系我們
中文日韩,成人区视频,av网页观看
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-PLOD3/APC Conjugated antibody (bs-12732R-APC)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-12732R-APC
英文名稱 Rabbit Anti-PLOD3/APC Conjugated antibody
中文名稱 APC標記的賴氨酸羥化酶3抗體
別    名 2-oxoglutarate 5-dioxygenase 3; bone protein I; BP-I; LH3; Lysine hydroxylase 3; Lysyl hydroxylase 3; Plod3; PLOD3_HUMAN; Procollagen lysine,2 oxoglutarate 5 dioxygenase 3 precursor; Procollagen-lysine.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 細胞生物  免疫學  細胞膜蛋白  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 Mouse,  (predicted: Human, Rat, Dog, Pig, Cow, Horse, Rabbit, Sheep, )
產品應用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 82kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human PLOD3
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
The protein encoded by this gene is a membrane-bound homodimeric enzyme that is localized to the cisternae of the rough endoplasmic reticulum. The enzyme (cofactors iron and ascorbate) catalyzes the hydroxylation of lysyl residues in collagen-like peptides. The resultant hydroxylysyl groups are attachment sites for carbohydrates in collagen and thus are critical for the stability of intermolecular crosslinks. Some patients with Ehlers-Danlos syndrome type VIB have deficiencies in lysyl hydroxylase activity. [provided by RefSeq, Jul 2008]

Function:
Forms hydroxylysine residues in -Xaa-Lys-Gly- sequences in collagens. These hydroxylysines serve as sites of attachment for carbohydrate units and are essential for the stability of the intermolecular collagen cross-links.

Subcellular Location:
Rough endoplasmic reticulum membrane.

DISEASE:
Defects in PLOD3 are the cause of lysyl hydroxylase 3 deficiency (LH3 deficiency) [MIM:612394]; also known as bone fragility with contractures arterial rupture and deafness. LH3 deficiency is a connective tissue disorder. The syndrome is characterized by congenital malformations severely affecting many tissues and organs and revealing features of several collagen disorders, most of them involving COL2A1 (type II collagen). The findings suggest that the failure of lysyl hydroxylation and hydroxylysyl carbohydrate addition, which affects many collagens, is the molecular basis of this syndrome.

Similarity:
Contains 1 Fe2OG dioxygenase domain.

Database links:

Entrez Gene: 8985 Human

Entrez Gene: 26433 Mouse

Entrez Gene: 288583 Rat

Omim: 603066 Human

SwissProt: O60568 Human

SwissProt: Q9R0E1 Mouse

SwissProt: Q5U367 Rat

Unigene: 153357 Human

Unigene: 251003 Mouse

Unigene: 90152 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.ggggww.cn 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網安備110107000727號
主站蜘蛛池模板: 超碰狠狠爱 | 国产麻豆一区二区三区四区 | 办公室少妇激情呻吟a片在线观看 | 欧美久久综合网 | 青青草成人免费 | 国产tv一区 | 色欲A∨无码蜜臀AV免费播 | 区二区欧美性插b在线视频网站 | 成人在线中文字幕 | 极品久久久久久 | 国产精品岛国久久久久久久久红粉 | 国产一级免费视频 | 国产香蕉97碰碰久久人人九色 | 日日夜夜91 | 99久久国产综合精麻豆 | 日日猛噜噜狠狠扒开双腿小说 | 国模两腿玉门打开图无码 | 大地资源高清在线 | 国产欧美日韩高清在线不卡 | 成人一级片在线免费观看 | 国产精品1区2区3区在线观看 | 毛片毛片毛片毛片毛片 | 欧美日韩小视频 | 国产精品无码日韩欧 | 69网站在线观看 | 啊灬啊灬啊灬快灬深一区二区 | 日本韩国国产 | 一本大道香一蕉久 | 无码内射成人免费喷射 | 国产一区二区三区美女 | 日韩激情综合网 | 色小妹三区 | 大乳三级a做爰大乳视频 | 国产精品人妻99一区二区 | 免费a片在线网站大全 | 九色国产在线观看 | 中国黄色一片 | 国内精品伊人久久久久AV | 免费网站成人亚洲 | 欧美人妖aa1片 | 国产又粗又猛又爽的免费网站 |